Nakamura Yuya, Kai Yosuke, Ueno Rimpei, Suzuki Yoshikazu, Ochiai Masaya, Ishikawa Takamasa, Takai Yuki, Arai Shuhei, Asano Taku, Shinke Toshiro
Division of Cardiology, Department of Medicine, School of Medicine, Showa University, Tokyo, Japan.
Division of Cardiology, Department of Medicine, School of Medicine, Showa University, Tokyo, Japan.
JACC Case Rep. 2025 Jun 18;30(15):103784. doi: 10.1016/j.jaccas.2025.103784.
Ebstein anomaly (EA) is a rare congenital heart defect characterized by tricuspid valve malformation and severe tricuspid regurgitation. This poses challenges for conventional pacemaker implantation.
An 86-year-old man with EA, atrial fibrillation, complete atrioventricular block, and heart failure underwent Micra VR leadless pacemaker implantation. The right ventricular angiography was inadequate due to torrential tricuspid regurgitation, necessitating the use of advanced mapping technologies. CARTO electroanatomical mapping and CARTO UNIVU navigation systems facilitated precise placement in the midseptal apex. At 6 months, the pacing parameters remained stable, and the patient was symptom free.
This case illustrates how advanced mapping technologies combined with leadless pacemakers can address anatomical challenges in EA. It underscores the importance of integrating modern technologies for precise device placement and improved outcomes in complex congenital conditions.
埃布斯坦畸形(EA)是一种罕见的先天性心脏缺陷,其特征为三尖瓣畸形和严重的三尖瓣反流。这给传统起搏器植入带来了挑战。
一名86岁患有EA、心房颤动、完全性房室传导阻滞和心力衰竭的男性接受了Micra VR无导线起搏器植入。由于严重的三尖瓣反流,右心室血管造影不充分,需要使用先进的标测技术。CARTO电解剖标测和CARTO UNIVU导航系统有助于在室间隔中部顶点精确放置。6个月时,起搏参数保持稳定,患者无症状。
该病例说明了先进的标测技术与无导线起搏器相结合如何应对EA中的解剖学挑战。它强调了整合现代技术以实现精确设备放置并改善复杂先天性疾病治疗结果的重要性。