Gong Ke-Rui, Zheng Zhuo-Lin, Li Guo-Fu, Chen Jun-Mao
Department of Minimally Invasive Interventional, North China University of Science and Technology Affiliated Hospital, Tangshan 063000, Hebei Province, China.
World J Gastrointest Endosc. 2025 Jun 16;17(6):106347. doi: 10.4253/wjge.v17.i6.106347.
Situs inversus viscerum (SIV) is a rare autosomal recessive genetic disorder characterized a complete mirror-image organ reversal in the thoracic and abdominal cavities. Its low incidence presents considerable challenges in clinical diagnosis and treatment, especially concerning gastrointestinal endoscopic procedures.
Herein, we report a case of an 80-year-old male with choledocholithiasis and acute obstructive empyematous cholangitis. Imaging revealed total visceral inversion in the patient. Endoscopic retrograde cholangiopancreatography (ERCP) was successfully performed to remove the stones, resulting to substantial relief of clinical symptoms and gradual improvement of the patient's condition, leading to successful recovery and discharge.
Therapeutic ERCP is a safe and effective surgical option for patients with SIV. The main focus for successful ERCP in patients with SIV includes positioning adjustments during the surgical process and using the dual-guidewire technique for biliary cannulation.
内脏反位(SIV)是一种罕见的常染色体隐性遗传病,其特征是胸腔和腹腔内器官完全呈镜像反转。其低发病率给临床诊断和治疗带来了相当大的挑战,尤其是在胃肠内镜检查方面。
在此,我们报告一例80岁男性患者,患有胆总管结石和急性梗阻性化脓性胆管炎。影像学检查显示该患者存在全内脏反位。成功进行了内镜逆行胰胆管造影(ERCP)以取出结石,临床症状得到显著缓解,患者病情逐渐改善,最终成功康复出院。
治疗性ERCP对于SIV患者是一种安全有效的手术选择。SIV患者成功进行ERCP的主要要点包括手术过程中的体位调整以及使用双导丝技术进行胆管插管。