Dubost C, Soyer R, Chauvaud S
Arch Mal Coeur Vaiss. 1977 Apr;70(4):379-84.
The double outlet right ventricle is a rare malformation, and its surgical correction has been well defined. The authors present seven cases of double outflow of the right ventricle and stenosis of the pulmonary outflow. If the technical problems of those variants with a subaortic septal defect seem to have been overcome, those with a subpulmonary ventricular septal defect present a much more difficult problem. Of the seven cases presented, the authors report the death of one patient who had a right ventricle with a double outlet associated with pulmonary stenosis and a sub-pulmonary ventricular septal defect. The post-operative course of the other 6 patients, who had a subaortic ventricular septal defect, was simple. One patient suffered secondary dehiscence of the repaired septal defect, and was reoperated on. The maximum follow-up period has been 7 years.
右心室双出口是一种罕见的畸形，其手术矫正方法已明确。作者报告了7例右心室双出口合并肺动脉流出道狭窄的病例。对于伴有主动脉下室间隔缺损的这类变异型，其技术问题似乎已得到解决，但伴有肺动脉下室间隔缺损的病例则面临更困难的问题。在报告的7例病例中，作者报道了1例右心室双出口合并肺动脉狭窄及肺动脉下室间隔缺损的患者死亡。另外6例伴有主动脉下室间隔缺损的患者术后病程简单。1例患者出现修补的室间隔缺损继发性裂开，并再次接受手术。最长随访期为7年。
