Senga Y, Satomi Y, Fukuda M, Taguchi H, Murayama T, Yamada T, Matsushita K, Misugi K
Hinyokika Kiyo. 1985 Jun;31(6):1013-9.
A case of embryonal rhabdomyosarcoma of the left kidney is reported. A 16-year-old boy was admitted with the complaint of left abdominal pain and fever on January 6, 1983. Radiological examination showed a tumor of the left kidney; and, nephrectomy was performed. Histopathologically the entire tumor was composed of undifferentiated round cells. Diagnosis of embryonal rhabdomyosarcoma was made on the basis of special stains including immunohistochemical study with nervous tissue specific enolase. Although radiation and chemotherapy were performed postoperatively, the tumor recurred and the patient died on October 22, 1983. The problems of differential diagnosis of embryonal rhabdomyosarcoma from sarcomatous types of nephroblastoma, particularly rhabdoid tumor and other undifferentiated renal tumors were discussed. Fifteen rhabdomyosarcoma of the kidney including our case have been reported in the Japanese literature.
报告一例左肾胚胎性横纹肌肉瘤。一名16岁男孩于1983年1月6日因左腹痛和发热入院。放射学检查显示左肾有肿瘤;遂行肾切除术。组织病理学检查显示整个肿瘤由未分化的圆形细胞组成。根据包括神经组织特异性烯醇化酶免疫组化研究在内的特殊染色结果,诊断为胚胎性横纹肌肉瘤。尽管术后进行了放疗和化疗,但肿瘤仍复发,患者于1983年10月22日死亡。文中讨论了胚胎性横纹肌肉瘤与肾母细胞瘤肉瘤类型,特别是横纹肌样瘤和其他未分化肾肿瘤的鉴别诊断问题。日本文献中已报道包括本例在内的15例肾横纹肌肉瘤。