Meienberg O, Karbowski K
Dtsch Med Wochenschr. 1977 May 27;102(21):781-4. doi: 10.1055/s-0028-1105443.
Continuous myoclonus in a localised area of the body was observed in three patients. In two cases the myocloni sometimes developed into motor Jacksonian convulsions. All three patients had neurological signs on the same side as their continuous twitching indicating a lesion of the contralateral hemisphere. The surface EEG did not show changes which could be directly correlated with continuous convulsions in any of the cases. The cause was found to be a malformation of the hemisphere in one case, a recent encephalomalacia in the second and a severe hyperosomolar diabetic electrolyte imbalance in the third. Epilepsia partialis continua Kozevnikov differs from motor Jacksonian epilepsy in the continuous non-attack character and the absence of a "march of convulsions". Pathophysiologically they are both forms of focal cortical status epilepticus.
三名患者出现了身体局部区域的持续性肌阵挛。在两例中,肌阵挛有时会发展为运动性杰克逊癫痫发作。所有三名患者在其持续性抽搐同侧均有神经体征,提示对侧半球有病变。在任何病例中,表面脑电图均未显示出与持续性惊厥直接相关的变化。病因在一例中为半球畸形,第二例为近期脑软化,第三例为严重高渗性糖尿病电解质失衡。连续性部分性癫痫(Kozevnikov型)与运动性杰克逊癫痫的不同之处在于其持续性非发作特征以及无“惊厥进展”。从病理生理学角度来看,它们都是局灶性皮质癫痫持续状态的形式。