斯内登综合征：一例诊断方法及影像学回顾的病例报告。

Sneddon's syndrome: A case report with diagnostic approach and imaging review.

作者信息

Beyyato Soukaina, Yammouri Zineb, Ouazzani Hajar, Chaouche Ismail, Akammar Amal, El Bouardi Nizar, Haloua Meriem, Lamrani Moulay Youssef Alaoui, Maaroufi Mustapha, Boubbou Meryem, Alami Badreeddine

机构信息

Department of Radiology and Interventional Imaging, CHU Hassan II, FEZ, Sidi Mohammed Ben Abdellah University, Fes, Morocco.

Department of Radiology Mother and Child and Interventional Imaging, CHU Hassan II, FEZ, Sidi Mohammed Ben Abdellah University, Fes, Morocco.

出版信息

Radiol Case Rep. 2025 Jul 9;20(9):4856-4859. doi: 10.1016/j.radcr.2025.06.041. eCollection 2025 Sep.

DOI:10.1016/j.radcr.2025.06.041

PMID:40686793

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC12274741/

Abstract

Sneddon's syndrome is a rare thrombotic vasculopathy characterized by the association of livedo racemosa and ischemic cerebrovascular events, typically affecting young to middle-aged women. We report the case of a 41-year-old woman who presented with sudden right-sided hemiparesis, expressive aphasia, and a history of livedo racemosa. MRI revealed bilateral ischemic lesions and cortical atrophy, while autoimmune and thrombophilia workups were negative. This case emphasizes the importance of considering Sneddon's syndrome in young patients with recurrent strokes and livedo racemosa, and highlights the diagnostic value of MRI combined with clinical evaluation.

摘要

斯内登综合征是一种罕见的血栓性血管病，其特征为网状青斑与缺血性脑血管事件相关联，通常影响年轻至中年女性。我们报告一例41岁女性，她出现突发右侧偏瘫、表达性失语，并有网状青斑病史。磁共振成像（MRI）显示双侧缺血性病变和皮质萎缩，而自身免疫和易栓症检查均为阴性。该病例强调了在患有复发性中风和网状青斑的年轻患者中考虑斯内登综合征的重要性，并突出了MRI结合临床评估的诊断价值。