Mach Maciej, Ostrowski Tomasz, Rusin Mikolaj M, Maciąg Rafał, Sajdek Michał, Gałązka Zbigniew
Department of General, Vascular, Endocrine and Transplant Surgery, Medical University of Warsaw, Warsaw, POL.
Centre of Radiological Diagnostics, National Medical Institute of the Ministry of the Interior and Administration, Warsaw, POL.
Cureus. 2025 Jul 21;17(7):e88411. doi: 10.7759/cureus.88411. eCollection 2025 Jul.
Median arcuate ligament syndrome (MALS), also known as Dunbar syndrome, is a rare vascular condition caused by compression of the celiac trunk by the median arcuate ligament, leading to altered visceral blood flow and promoting collateral circulation that can predispose patients to visceral artery aneurysms (VAAs), particularly within the pancreaticoduodenal arcade. These aneurysms carry a significant risk of rupture and require timely intervention. We present the case of a 75-year-old female patient with an incidentally discovered large superior mesenteric artery (SMA) aneurysm and complete celiac trunk occlusion due to MALS. The patient's medical history was notable for multiple comorbidities and bilateral hip arthroplasties, which rendered magnetic resonance imaging (MRI) nonviable because of pronounced metal artifacts. Over a period of six years, she underwent several staged endovascular embolization procedures using detachable coils via various arterial access points. Despite initial technical success, imaging follow-up was compromised by artifacts from orthopedic implants and embolization materials, limiting precise assessment of the aneurysm. Residual perfusion and recanalization within the aneurysm sac necessitated repeated interventions. The patient declined surgical treatment, restricting therapeutic options and prompting continued conservative monitoring. This case illustrates the complexity of managing large visceral artery aneurysms in the context of MALS and altered vascular anatomy, particularly when imaging capabilities are limited. The inability to perform MRI significantly impacted optimal follow-up and required reliance on artifact-prone options such as Doppler ultrasound and computed tomography angiography (CTA). These limitations, coupled with the patient's refusal of surgery, highlight the importance of individualized treatment approaches, multidisciplinary collaboration, and transparent patient communication regarding therapeutic options, risks, and constraints. Endovascular management of complex SMA aneurysms associated with MALS is feasible but presents significant diagnostic and therapeutic challenges. Successful outcomes in such cases depend on careful procedural planning, selection of appropriate imaging techniques, and shared decision-making tailored to patient-specific anatomical and clinical factors.
正中弓状韧带综合征(MALS),也称为邓巴综合征,是一种罕见的血管疾病,由正中弓状韧带压迫腹腔干引起,导致内脏血流改变并促进侧支循环形成,使患者易患内脏动脉瘤(VAA),尤其是在胰十二指肠动脉弓内。这些动脉瘤破裂风险很高,需要及时干预。我们报告一例75岁女性患者,因MALS偶然发现巨大的肠系膜上动脉(SMA)动脉瘤和腹腔干完全闭塞。患者有多种合并症和双侧髋关节置换术病史,由于明显的金属伪影,磁共振成像(MRI)无法进行。在六年的时间里,她通过不同的动脉入路点,使用可脱卸线圈接受了多次分期血管内栓塞手术。尽管最初技术成功,但影像学随访受到骨科植入物和栓塞材料伪影的影响,限制了对动脉瘤的精确评估。动脉瘤腔内的残余灌注和再通需要反复干预。患者拒绝手术治疗,限制了治疗选择,促使继续进行保守监测。该病例说明了在MALS和血管解剖结构改变的情况下,处理巨大内脏动脉瘤的复杂性,特别是当成像能力有限时。无法进行MRI对最佳随访产生了重大影响,需要依赖诸如多普勒超声和计算机断层血管造影(CTA)等容易产生伪影的检查方法。这些限制,再加上患者拒绝手术,凸显了个体化治疗方法、多学科协作以及就治疗选择、风险和限制与患者进行透明沟通的重要性。与MALS相关的复杂SMA动脉瘤的血管内治疗是可行的,但存在重大的诊断和治疗挑战。此类病例的成功结果取决于仔细的手术规划、选择合适的成像技术以及根据患者特定的解剖和临床因素进行共同决策。