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小儿先天性胆管扩张症合并胆管穿孔的急诊一期机器人手术:一例报告

Emergency One-Stage Robotic Surgery for Congenital Biliary Dilatation With Bile Duct Perforation in a Pediatric Patient: A Case Report.

作者信息

Asai Hajime, Shirota Chiyoe, Tainaka Takahisa, Makita Satoshi, Ogawa Katsuhiro, Okamoto Masamune, Yasui Akihiro, Takada Shunya, Hayashi Kaito, Nakagawa Yoichi, Katou Daiki, Ishii Hiroki, Utsunomiya Ami, Uchida Hiroo

机构信息

Department of Pediatric Surgery, Nagoya University Graduate School of Medicine, Nagoya, Japan.

出版信息

Asian J Endosc Surg. 2025 Jan-Dec;18(1):e70122. doi: 10.1111/ases.70122.

DOI:10.1111/ases.70122
PMID:40695451
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC12283185/
Abstract

Bile duct perforation is a rare, serious complication of congenital biliary dilatation (CBD). While traditionally managed with a two-stage surgical approach, recent reports suggest that one-stage, minimally invasive approaches may be feasible. We present the case of a 13-month-old female who developed bile duct perforation associated with a protein plug in the common channel. Following the correction of coagulopathy, emergency robotic surgery was performed, including bile duct excision and Roux-en-Y hepaticojejunostomy. Despite significant adhesions and an anatomical anomaly in which the right hepatic artery coursed anterior to the common hepatic duct, robotic dissection and reconstruction were safely completed. The postoperative course was uneventful, and the patient was discharged. This report highlights the feasibility and potential advantages of one-stage robotic surgery for CBD with perforation, even in the presence of active inflammation and vascular anomalies. Similar cases must be reported and evaluated to understand the indications and limitations of this approach.

摘要

胆管穿孔是先天性胆管扩张症(CBD)一种罕见的严重并发症。传统上采用两阶段手术方法进行治疗,但最近的报告表明,一期微创方法可能是可行的。我们报告一例13个月大的女性患者,其发生与共同通道内蛋白栓相关的胆管穿孔。在纠正凝血功能障碍后,进行了急诊机器人手术,包括胆管切除和Roux-en-Y肝空肠吻合术。尽管存在严重粘连以及右肝动脉走行于肝总管前方的解剖异常,但机器人手术分离和重建仍安全完成。术后过程顺利,患者出院。本报告强调了一期机器人手术治疗穿孔性CBD的可行性和潜在优势,即使存在活动性炎症和血管异常。必须报告和评估类似病例,以了解该方法的适应证和局限性。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4842/12283185/a446e0bdc888/ASES-18-e70122-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4842/12283185/d95b79c1491b/ASES-18-e70122-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4842/12283185/9b622c5c9e46/ASES-18-e70122-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4842/12283185/a446e0bdc888/ASES-18-e70122-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4842/12283185/d95b79c1491b/ASES-18-e70122-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4842/12283185/9b622c5c9e46/ASES-18-e70122-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/4842/12283185/a446e0bdc888/ASES-18-e70122-g003.jpg

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本文引用的文献

1
Safety and feasibility of robot-assisted surgery for pediatric patients weighing ≤ 10 kg with congenital biliary dilatation.机器人辅助手术用于体重≤10kg的先天性胆管扩张症儿科患者的安全性和可行性。
J Robot Surg. 2024 Dec 27;19(1):34. doi: 10.1007/s11701-024-02181-5.
2
Robotic versus laparoscopic radical surgery for pediatric congenital biliary dilatation: a comparison of surgical outcomes of a single surgeon's initial experience.机器人与腹腔镜根治术治疗小儿先天性胆管扩张症:单外科医生初始经验的手术结果比较。
Pediatr Surg Int. 2023 Sep 3;39(1):261. doi: 10.1007/s00383-023-05548-1.
3
Ruptured choledochal cyst: One-stage or two-stage, open or laparoscopic surgery?
胆总管囊肿破裂:一期手术还是二期手术,开放手术还是腹腔镜手术?
J Minim Access Surg. 2023 Jan-Mar;19(1):138-140. doi: 10.4103/jmas.jmas_206_21.
4
Efficacy of robot-assisted hepaticojejunostomy and laparoscopic-assisted hepaticojejunostomy in pediatric congenital choledochal dilatation: a system review and meta-analysis.机器人辅助胆肠吻合术和腹腔镜辅助胆肠吻合术治疗小儿先天性胆总管扩张的疗效:系统评价和荟萃分析。
Pediatr Surg Int. 2022 Dec 11;39(1):46. doi: 10.1007/s00383-022-05286-w.
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Surgical outcomes of robotic-assisted cyst excisions and hepaticojejunostomies in patients with perforated choledochal cysts: a single-center retrospective study.机器人辅助胆囊切除术和胆肠吻合术治疗穿孔性胆总管囊肿患者的手术结果:单中心回顾性研究。
Updates Surg. 2023 Apr;75(3):571-580. doi: 10.1007/s13304-022-01435-x. Epub 2022 Nov 28.
6
One- versus two-stage single-incision laparoscopic cyst excision and hepaticojejunostomy in patients with completely perforated choledochal cysts and good medical conditions.对于完全穿孔的胆总管囊肿且身体状况良好的患者,行一期或两期经单切口腹腔镜胆囊切除术和胆肠吻合术。
Pediatr Surg Int. 2022 Apr;38(4):541-545. doi: 10.1007/s00383-022-05073-7. Epub 2022 Feb 14.
7
Single-stage operation for perforated choledochal cyst.胆管囊肿穿孔的一期手术
J Pediatr Surg. 2018 Apr;53(4):653-655. doi: 10.1016/j.jpedsurg.2017.07.014. Epub 2017 Jul 21.
8
Drainage-related Complications in Percutaneous Transhepatic Biliary Drainage: An Analysis Over 10 Years.经皮肝穿刺胆道引流术相关引流并发症:十年分析
J Clin Gastroenterol. 2015 Oct;49(9):764-70. doi: 10.1097/MCG.0000000000000275.
9
One-staged or two-staged surgery for perforated choledochal cyst with bile peritonitis in children? A single center experience with 27 cases.儿童胆总管囊肿穿孔伴胆汁性腹膜炎的一期或二期手术?单中心27例经验
Pediatr Surg Int. 2014 Mar;30(3):287-90. doi: 10.1007/s00383-014-3461-6.