WHIM综合征中的单克隆丙种球蛋白病可掩盖低丙种球蛋白血症。
Monoclonal gammopathy in WHIM syndrome can mask hypogammaglobulinemia.
作者信息
Lew Julia, Adatia Adil
机构信息
Department of Pediatrics, University of Toronto, Toronto, Ontario.
Division of Pulmonary Medicine, Department of Medicine, University of Alberta, Edmonton, Alberta, Canada.
出版信息
J Allergy Clin Immunol Glob. 2025 Jun 24;4(3):100526. doi: 10.1016/j.jacig.2025.100526. eCollection 2025 Aug.
Abstract
Monoclonal gammopathy can be seen at an early age in patients with warts-hypogammaglobulinemia, infections, and myelokathexis syndrome and can mask the presence of hypogammaglobulinemia.
摘要
在患有疣状低丙种球蛋白血症、感染和髓细胞滞留综合征的患者中，单克隆丙种球蛋白病可在早年出现，并可掩盖低丙种球蛋白血症的存在。
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