Parcheta B, Wisniewski L, Piontek E, Szymanska J, Skawinski W, Wermenski K
Eur J Pediatr. 1985 Nov;144(4):409-12. doi: 10.1007/BF00441791.
A 30-month-old boy with severe psychomotor retardation and numerous developmental anomalies, such as small trigonocephalic head, craniofacial anomalies, malformations of fingers with hypoplastic thumbs, anomalies of urogenital organs and imperforate anus, is presented. Cytogenetic studies of peripheral blood lymphocytes with differential staining of chromosomes revealed 46,XY,r13 karyotype. The correlation between clinical features and the observed chromosome aberration is discussed. Hitherto unreported developmental brain anomalies with partial exhibited skeletal abnormalities, some not reported previously.
本文介绍了一名30个月大的男孩,他患有严重的精神运动发育迟缓以及众多发育异常,如小头畸形、颅面畸形、伴有拇指发育不全的手指畸形、泌尿生殖器官异常和肛门闭锁。对周围血淋巴细胞进行染色体鉴别染色的细胞遗传学研究显示其核型为46,XY,r13。文中讨论了临床特征与观察到的染色体畸变之间的相关性。此前未报道过的发育性脑异常伴有部分骨骼异常,其中一些以前未曾报道过。