Foasso M F, Hermier M, David M, Duquesnel J, Tommasi M
Arch Fr Pediatr. 1985 Nov;42(9):791-4.
The authors report what seems to be the 4th case of acute pseudotumoral demyelinating disease with regressive evolution. Onset was marked by hemiplegia with tumoral pattern on CAT-scan and pneumoencephalography and an important cystic cavity at surgery. Controlateral hemiplegia occurred 2 months later. After a period of partial recovery a long period of remission was observed, followed by a relapse 10 years after the first symptoms. This case suggests that remissions reaching 10 years are possible in such pseudotumoral demyelinating disease, but also shows that there are late secondary evolutions, as in multiple sclerosis.
作者报告了似乎是第4例具有退行性演变的急性假瘤性脱髓鞘疾病。起病表现为偏瘫，CT扫描和气脑造影显示有肿瘤样表现，手术时发现一个重要的囊性腔隙。2个月后出现对侧偏瘫。经过一段时间的部分恢复后，观察到长期缓解，在首次出现症状10年后复发。该病例表明，这种假瘤性脱髓鞘疾病可能出现长达10年的缓解期，但也显示出存在晚期继发演变，如同多发性硬化症一样。
