Suppr超能文献

自婴儿期起的慢性紫绀:揭示巨大的右肺动静脉畸形。

Chronic cyanosis since infancy: Unveiling a giant right pulmonary arteriovenous malformation.

作者信息

Komala Dian, Nugraha Harry Galuh, Ramadhan Firman, Khairuddin Rais, Kuswiyanto Rahmat Budi, Apandi Putria Rayani

机构信息

Department of Radiology, Faculty of Medicine, Universitas Padjadjaran, West Java, Indonesia.

Department of Pediatric, Faculty of Medicine, Universitas Padjadjaran, West Java, Indonesia.

出版信息

Radiol Case Rep. 2025 Aug 5;20(10):5353-5356. doi: 10.1016/j.radcr.2025.06.084. eCollection 2025 Oct.

Abstract

Giant pulmonary arteriovenous malformations (PAVMs) are rare vascular anomalies involving direct connections between pulmonary arteries and veins, leading to right-to-left shunting and systemic hypoxemia. While small PAVMs may be asymptomatic, larger lesions often present with dyspnea, cyanosis, and related complications. An 18-year-old female with progressive dyspnea and cyanosis-first noted during infancy-was found to have a giant PAVM in the right lower lung lobe on thoracic computed tomography (CT). Imaging, particularly computed tomography (CT), was essential for diagnosis and treatment planning. This case underscores the need to consider PAVMs in the differential diagnosis of chronic cyanosis and highlights the critical role of radiologists in identifying and characterizing these lesions to guide appropriate management.and characterizing these lesions to support optimal clinical decision-making.

摘要

巨大肺动静脉畸形(PAVM)是一种罕见的血管异常,涉及肺动脉和静脉之间的直接连接,导致右向左分流和全身性低氧血症。虽然小型PAVM可能无症状,但较大的病变通常表现为呼吸困难、发绀及相关并发症。一名18岁女性,自幼出现进行性呼吸困难和发绀,胸部计算机断层扫描(CT)发现右下肺叶有巨大PAVM。影像学检查,尤其是计算机断层扫描(CT),对诊断和治疗规划至关重要。该病例强调了在慢性发绀的鉴别诊断中需要考虑PAVM,并突出了放射科医生在识别和描述这些病变以指导适当管理方面的关键作用,以及描述这些病变以支持最佳临床决策的关键作用。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a475/12365801/b22733eeffa9/gr1.jpg

相似文献

本文引用的文献

1
Complex Pulmonary Arteriovenous Fistula Presented With Ventricular Tachycardia and Type 2 Acute Myocardial Infarction.
Cureus. 2024 May 30;16(5):e61347. doi: 10.7759/cureus.61347. eCollection 2024 May.
2
Epidemiology of giant cell arteritis in Waikato, Aotearoa New Zealand.
N Z Med J. 2024 Mar 22;137(1592):14-21. doi: 10.26635/6965.6379.
4
Preliminary Experience with a Low-Profile High-Density Braid Occluder for Transcatheter Embolization of Pulmonary Arteriovenous Malformations.
J Vasc Interv Radiol. 2024 Jan;35(1):32-35.e2. doi: 10.1016/j.jvir.2023.09.016. Epub 2023 Sep 23.
5
Update on pulmonary arteriovenous malformations.
J Bras Pneumol. 2023 May 1;49(2):e20220359. doi: 10.36416/1806-3756/e20220359. eCollection 2023.
9
Ischemic stroke due to sporadic and genetic pulmonary arteriovenous malformations: Case report.
Brain Circ. 2022 Mar 21;8(1):57-60. doi: 10.4103/bc.bc_66_21. eCollection 2022 Jan-Mar.
10
Diagnosis and endovascular management of pulmonary arteriovenous malformations.
Br J Radiol. 2021 Jul 1;94(1123):20200695. doi: 10.1259/bjr.20200695. Epub 2021 May 26.

文献AI研究员

20分钟写一篇综述,助力文献阅读效率提升50倍。

立即体验

用中文搜PubMed

大模型驱动的PubMed中文搜索引擎

马上搜索

文档翻译

学术文献翻译模型,支持多种主流文档格式。

立即体验