Bardooli Fawaz, Aljawder Dhuha Rashed, Kumar Dileep, Shivappa Sadananda Padavagodu, Baritussio Anna
Mohammed Bin Khalifa Specialist Cardiac Centre, Awali, Bahrain, UAE.
Department of Cardiology, Phoenix Hospital (Ahalia), Mussafah, Abu Dhabi, UAE.
Heart Views. 2025 Jan-Mar;26(1):48-53. doi: 10.4103/heartviews.heartviews_145_24. Epub 2025 Jul 16.
Arrhythmogenic cardiomyopathy (AC) is an inherited heart disease characterized by fibro-fatty changes of either ventricles in isolation or in combination. AC may present with ventricular tachycardia (VT), usually with a left bundle branch block (LBBB) morphology (although VT with right bundle branch block morphology may also be encountered). Diagnosis is multi-parametric and cardiovascular magnetic resonance (CMR) holds a key role in showing the typical tissue abnormalities of the ventricles. We report the case of a patient presenting with LBBB VT with multi-modality imaging findings consistent with AC with biventricular involvement and right ventricular (RV) thrombosis. The patient was treated with antiarrhythmics, heart failure therapy, and implantable cardioverter-defibrillator implantation. RV thrombus was treated with new oral anticoagulants.
致心律失常性心肌病（AC）是一种遗传性心脏病，其特征为孤立或合并出现的心室纤维脂肪变性。AC可能表现为室性心动过速（VT），通常呈左束支传导阻滞（LBBB）形态（尽管也可能遇到右束支传导阻滞形态的VT）。诊断是多参数的，心血管磁共振成像（CMR）在显示心室典型组织异常方面起着关键作用。我们报告了一例表现为LBBB VT的患者，其多模态影像学检查结果符合双心室受累及右心室（RV）血栓形成的AC。该患者接受了抗心律失常药物、心力衰竭治疗以及植入式心脏复律除颤器植入治疗。RV血栓采用新型口服抗凝剂进行治疗。
