Acharya Ramesh, Gutierrez-Sierra Gerardo, Prakash Vishakh, Acharya Suchita, Murali Sandesh, Abolbashari Mehran
Department of Internal Medicine, Texas Tech University Health Sciences Center El Paso, Paul L. Foster School of Medicine, The Hospitals of Providence-Transmountain, El Paso, TX, USA.
Department of Cardiovascular Medicine, Center of the Heart, El Paso, TX, USA.
Am J Case Rep. 2025 Aug 28;26:e948875. doi: 10.12659/AJCR.948875.
BACKGROUND Apical hypertrophic cardiomyopathy (ApHCM) is a rare variant that is less frequently associated with sarcomere mutations and lacks specific diagnosis and risk stratification guidelines. CASE REPORT We present the case of a 41-year-old man with a complex medical history, including type I diabetes mellitus and alcohol use disorder, who presented with nausea and vomiting following alcohol consumption. Initial evaluations revealed significant electrolyte imbalances and non-sustained ventricular tachycardia (NSVT). Echocardiography indicated severe apical hypertrophy consistent with ApHCM. The patient developed polymorphic ventricular tachycardia, which progressed to ventricular fibrillation (VF), necessitating cardiopulmonary resuscitation (CPR) and intensive care. An implantable cardioverter-defibrillator (ICD) was successfully implanted for secondary prevention. CONCLUSIONS This report focuses on the clinical presentation and management of ApHCM, emphasizing the challenges of arrhythmogenic risks and the potential for refractory ventricular arrhythmias. Surgical interventions, such as apical myectomy, can improve functional capacity. This case underscores the critical need for tailored management strategies in patients with ApHCM, particularly in those with substance use disorders, where standard therapies may be contraindicated.
心尖肥厚型心肌病(ApHCM)是一种罕见的变异型,与肌节突变的相关性较低,且缺乏特定的诊断和风险分层指南。
我们报告一例41岁男性患者,其有复杂的病史,包括I型糖尿病和酒精使用障碍,在饮酒后出现恶心和呕吐。初始评估发现严重的电解质失衡和非持续性室性心动过速(NSVT)。超声心动图显示严重的心尖肥厚,符合ApHCM。患者发展为多形性室性心动过速,进而进展为心室颤动(VF),需要进行心肺复苏(CPR)和重症监护。成功植入植入式心脏复律除颤器(ICD)用于二级预防。
本报告重点关注ApHCM的临床表现和管理,强调致心律失常风险的挑战以及难治性室性心律失常的可能性。手术干预,如心尖心肌切除术,可以改善功能能力。该病例强调了对ApHCM患者制定个性化管理策略的迫切需求,特别是在患有物质使用障碍的患者中,因为标准疗法可能是禁忌的。