一名6岁男孩双侧桡侧多指（趾）畸形在低收入国家接受尺桡骨融合术治疗。病例报告。
Bilateral radial clubhand in a 6-year-old boy treated with ulnar radialization in a low-income country. A case report.
作者信息
Ranaivoson Manitr''Oliva Iarimanalina, Daoulas Thomas, Maincourt Pierre, Manasse Rakotoherisoa Herijaona, Anesy Christophane Als Anselme, Ralahy Malinirina Fanjalalaina
机构信息
Pediatric Surgery Department, Andrainjato Fianarantsoa University Hospital, Madagascar.
Orthopedic Surgery Department, Cavale Blanche University Hospital, 29200 Brest, France.
出版信息
Int J Surg Case Rep. 2025 Oct;135:111860. doi: 10.1016/j.ijscr.2025.111860. Epub 2025 Aug 21.
INTRODUCTION
Radial club hand is a rare congenital malformation with functional and aesthetic repercussions.
PRESENTATION OF CASE
We present the case of a 6-year-old boy with bilateral hand deformity, associated with hypoplasia of the thenar muscles and aplasia of the radius (Bayne stage IV). After bilateral ulnar radialisation, recovery was favorable, with stability of the hand axis and a fine grip allowing writing. At 18 months postoperatively, the child was able to integrate into school without assistance.
DISCUSSION
Radial clubhands are rare malformations, often treated late in Madagascar due to a lack of resources. Despite these challenges, simple techniques like ulnar radialization can achieve excellent outcomes with minimal equipment.
CONCLUSION
Surgery remains essential, even in cases treated late.
引言
桡侧多指畸形是一种罕见的先天性畸形，会对功能和美观产生影响。
病例介绍
我们报告一例6岁男孩，患有双侧手部畸形，伴有大鱼际肌发育不全和桡骨缺如（Bayne Ⅳ期）。双侧尺骨桡侧化术后，恢复情况良好，手轴稳定，抓握精细，能够写字。术后18个月，患儿能够无需帮助融入学校生活。
讨论
桡侧多指畸形较为罕见，在马达加斯加，由于资源匮乏，此类畸形常常得不到及时治疗。尽管存在这些挑战，但像尺骨桡侧化这样的简单技术，只需最少的设备就能取得出色的治疗效果。
结论
即使是治疗较晚的病例，手术仍然至关重要。
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