Ozaki Kensuken, Oshima Susumu, Tomohiro Hirokami, Shigeru Sakurai
Kawasaki Aortic Center, Kawasaki Saiwai Hospital, Kawasaki, Japan.
Multimed Man Cardiothorac Surg. 2025 Sep 5;2025. doi: 10.1510/mmcts.2025.088.
Kommerell's diverticulum (KD) combined with a right-sided aortic arch (RAA) and an aberrant left subclavian artery (ALSA) is a rare congenital vascular anomaly causing significant compressive dysphagia. Treatment options, including open surgery, thoracic endovascular aortic repair and hybrid approaches, are debated due to anatomical complexities. We report a 48-year-old female with dysphagia from symptomatic KD, RAA and ALSA, clearly delineated by preoperative computed tomography angiography. A right thoracotomy enabled aortic arch replacement. Deep hypothermic circulatory arrest and retrograde cerebral perfusion were utilized for neuroprotection. KD was resected, and ALSA was reconstructed via interposition graft, anastomosed end-to-side to the main prosthetic graft. Meticulous dissection, including division of the ligament on the diverticulum's greater curvature, and careful handling of fragile aortic tissue with felt-pledgeted sutures were key. The patient recovered uneventfully, with complete dysphagia resolution and discharge on postoperative Day 10, without complications. Right thoracotomy offers excellent exposure for comprehensive repair of complex KD with RAA and ALSA. This case demonstrates the feasibility and effectiveness of open surgical repair with meticulous technique and cerebral protection for favourable outcomes in such rare and challenging vascular anomalies.
科默雷尔憩室(KD)合并右侧主动脉弓(RAA)和迷走左锁骨下动脉(ALSA)是一种罕见的先天性血管异常,可导致严重的压迫性吞咽困难。由于解剖结构复杂,包括开放手术、胸主动脉腔内修复术和杂交手术等治疗方案仍存在争议。我们报告一例48岁女性,因有症状的KD、RAA和ALSA出现吞咽困难,术前计算机断层扫描血管造影清晰显示了病变情况。通过右胸切开术进行主动脉弓置换。采用深低温停循环和逆行脑灌注进行神经保护。切除KD,并通过植入移植物重建ALSA,将其端侧吻合至主人工血管移植物。细致的解剖操作,包括切断憩室大弯侧的韧带,以及用带垫片缝线小心处理脆弱的主动脉组织是关键。患者恢复顺利,吞咽困难完全缓解,术后第10天出院,无并发症。右胸切开术为复杂的KD合并RAA和ALSA的全面修复提供了良好的暴露。本病例证明了采用细致技术和脑保护的开放手术修复在这种罕见且具有挑战性的血管异常中取得良好结果的可行性和有效性。