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常规术前评估中发现的无症状性心尖肥厚型心肌病

Asymptomatic Apical Hypertrophic Cardiomyopathy Uncovered During Routine Preoperative Evaluation.

作者信息

Strickland Emily, Arrey-Mbi Takor B

机构信息

Internal Medicine, Madigan Army Medical Center, Tacoma, USA.

Medicine/Cardiology, Madigan Army Medical Center, Tacoma, USA.

出版信息

Cureus. 2025 Aug 4;17(8):e89362. doi: 10.7759/cureus.89362. eCollection 2025 Aug.

DOI:10.7759/cureus.89362
PMID:40918890
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC12409759/
Abstract

Apical hypertrophic cardiomyopathy (ApHCM) is an uncommon, nonobstructive form of hypertrophic cardiomyopathy (HCM) that is associated with an increased risk of ventricular aneurysms, atrial fibrillation, heart failure, and cardiac death. In this case report, a 63-year-old male patient was found to have deeply negative T waves on electrocardiogram (EKG) during a routine preoperative evaluation in an outpatient internal medicine clinic. Imaging with echocardiography and cardiac magnetic resonance confirmed the diagnosis of ApHCM. Once the diagnosis was made, the patient underwent a thorough, guideline-directed evaluation for risk of sudden cardiac death (SCD), including ambulatory cardiac monitoring, cardiac MRI, and genetic testing. The patient continues to receive longitudinal care, including medical therapies with a beta-blocker, and periodic follow-up assessments of SCD risk.

摘要

心尖肥厚型心肌病(ApHCM)是肥厚型心肌病(HCM)的一种罕见的非梗阻性形式,与心室壁瘤、心房颤动、心力衰竭和心源性死亡风险增加相关。在本病例报告中,一名63岁男性患者在门诊内科诊所进行常规术前评估时,心电图(EKG)显示T波深倒置。超声心动图和心脏磁共振成像检查确诊为ApHCM。确诊后,对该患者进行了全面的、遵循指南的心脏性猝死(SCD)风险评估,包括动态心脏监测、心脏磁共振成像和基因检测。该患者继续接受长期护理,包括使用β受体阻滞剂进行药物治疗,以及定期进行SCD风险的随访评估。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f3b3/12409759/a954f75debb3/cureus-0017-00000089362-i03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f3b3/12409759/4f82015bc9cd/cureus-0017-00000089362-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f3b3/12409759/20e494bdd766/cureus-0017-00000089362-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f3b3/12409759/a954f75debb3/cureus-0017-00000089362-i03.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f3b3/12409759/4f82015bc9cd/cureus-0017-00000089362-i01.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f3b3/12409759/20e494bdd766/cureus-0017-00000089362-i02.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f3b3/12409759/a954f75debb3/cureus-0017-00000089362-i03.jpg

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本文引用的文献

1
2020 AHA/ACC Guideline for the Diagnosis and Treatment of Patients With Hypertrophic Cardiomyopathy: A Report of the American College of Cardiology/American Heart Association Joint Committee on Clinical Practice Guidelines.2020年美国心脏协会/美国心脏病学会肥厚型心肌病患者诊断和治疗指南:美国心脏病学会/美国心脏协会临床实践指南联合委员会报告
J Am Coll Cardiol. 2020 Dec 22;76(25):e159-e240. doi: 10.1016/j.jacc.2020.08.045. Epub 2020 Nov 20.
2
Apical Hypertrophic Cardiomyopathy: The Variant Less Known.心尖肥厚型心肌病:鲜为人知的变异型
J Am Heart Assoc. 2020 Mar 3;9(5):e015294. doi: 10.1161/JAHA.119.015294. Epub 2020 Feb 28.
3
Risk of death in long-term follow-up of patients with apical hypertrophic cardiomyopathy.
心尖肥厚型心肌病患者长期随访的死亡风险。
Am J Cardiol. 2013 Jun 15;111(12):1784-91. doi: 10.1016/j.amjcard.2013.02.040. Epub 2013 Mar 27.
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Comparison of prevalence of apical hypertrophic cardiomyopathy in Japan and the United States.日本与美国肥厚型心肌病患病率的比较。
Am J Cardiol. 2003 Nov 15;92(10):1183-6. doi: 10.1016/j.amjcard.2003.07.027.