Optic Nerve Head Pigmentation: Case Report and Literature Review.

We describe a case of unilateral sectoral pigmentation of the optic disc in a healthy 58‑year‑old female who presented with decreased vision and visual field defect in the involved eye since childhood. The patient was initially diagnosed with melanocytoma of the optic nerve given the suggestive clinical appearance. Thorough assessment with magnetic resonance imaging studies, laboratory work-ups and ophthalmic examination indicated that the pigmentation was linked to optic nerve hypoplasia.