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处女膜闭锁合并阴道尿道瘘

Imperforate vagina with vaginourethral communication.

作者信息

Kirks D R, Currarino G

出版信息

AJR Am J Roentgenol. 1977 Oct;129(4):623-8. doi: 10.2214/ajr.129.4.623.

DOI:10.2214/ajr.129.4.623
PMID:409234
Abstract

Six female children are described with an unusual congenital anomaly characterized by imperforate vagina with otherwise normal external genitalia as well as communication between the proximal patent vagina and a normal female urethra. This abnormality was associated with hydrometrocolpos at birth in two patients. The anomaly may embryologically be related to the primitive urogenital sinus.

摘要

本文描述了6名女童患有一种罕见的先天性异常,其特征为阴道闭锁,而外阴其他部分正常,且近端通畅的阴道与正常女性尿道之间存在连通。两名患者出生时伴有阴道积血和子宫积血。从胚胎学角度来看,这种异常可能与原始泌尿生殖窦有关。

相似文献

1
Imperforate vagina with vaginourethral communication.处女膜闭锁合并阴道尿道瘘
AJR Am J Roentgenol. 1977 Oct;129(4):623-8. doi: 10.2214/ajr.129.4.623.
2
Persistent urogenital sinus: prenatal diagnosis and pregnancy complications.持续性泌尿生殖窦:产前诊断与妊娠并发症
Am J Obstet Gynecol. 1997 Mar;176(3):709-11. doi: 10.1016/s0002-9378(97)70575-1.
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Clinical evaluation of imperforate anus: clue to type of anal-rectal anomaly.肛门闭锁的临床评估:肛门直肠畸形类型的线索
AJR Am J Roentgenol. 1979 Aug;133(2):289-92. doi: 10.2214/ajr.133.2.289.
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Primary vaginal calculus secondary to urethrovaginal fistula with imperforate hymen in a 6-year-old girl.一名6岁女童因处女膜闭锁合并尿道阴道瘘继发原发性阴道结石。
J Pediatr Surg. 2009 Jul;44(7):e11-3. doi: 10.1016/j.jpedsurg.2009.03.040.
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Hydronephrosis secondary to vaginal atresia.阴道闭锁继发肾积水。
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Duplication of the colon: varied presentations of a rare congenital anomaly.结肠重复畸形:一种罕见先天性异常的多样表现
Can Assoc Radiol J. 1988 Mar;39(1):29-32.
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Partial vaginal agenesis with a urinary-vaginal fistula.
Obstet Gynecol. 1981 Jul;58(1):130-4.
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Hydrocolpos, vaginal atresia, and urethrovaginal fistula in a neonate: abdomino-perineal-vaginal pull-through.新生儿的阴道积水、阴道闭锁和尿道阴道瘘:腹会阴阴道拖出术
J Pediatr Surg. 1977 Aug;12(4):605-7. doi: 10.1016/0022-3468(77)90210-x.
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Anatomical measurements of the urogenital sinus in virilized female children due to congenital adrenal hyperplasia.先天性肾上腺增生所致男性化女童泌尿生殖窦的解剖学测量
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Congenital urethrovaginal fistula with transverse vaginal septum.先天性尿道阴道瘘伴阴道横隔
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引用本文的文献

1
Symptomatic urinary problems in female genital tract anomalies.女性生殖道畸形中的症状性泌尿系统问题。
Int Urogynecol J Pelvic Floor Dysfunct. 2009 Apr;20(4):401-6. doi: 10.1007/s00192-008-0783-8. Epub 2008 Dec 18.
2
Pallister-Hall syndrome and McKusick-Kaufmann syndrome: one entity?帕利斯特-霍尔综合征和麦库西克-考夫曼综合征:是同一实体吗?
J Med Genet. 1995 Feb;32(2):125-8. doi: 10.1136/jmg.32.2.125.