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法洛四联症矫正手术的结果。

Results of corrective surgery for tetralogy of Fallot.

作者信息

Hruda J, Samánek M, Hucín B, First T, Reich O, Vorísková M, Zapletal A, Tláskal T, Skovránek J

出版信息

Cor Vasa. 1985;27(6):426-33.

PMID:4092472
Abstract

During a 5-year period (1978-1983) corrective surgery for tetralogy of Fallot was performed in 114 patients, ranging in age from 2 to 24 years (mean 8.4 years). Forty-one of them (35.9%) had previously undergone a palliative operation. Insertion of a transannular patch was necessary in 48 patients (42.1%). Eleven children died in the immediate postoperative period (early mortality 9.6%); no deaths occurred later. 103 survivors were followed-up for periods ranging from 5 months to 5 years mean 2.4 years) after surgery. The condition in 91 patients was excellent (88.7%), in 11 good (10.7%) and in one poor. Residual ventricular septal defect persisted in 9 patients (8.7%). Postoperative ECG revealed complete right bundle branch block in 71 patients (59%), incomplete block in 18 (18%), 5 patients (5%) had complete RBBB with left anterior hemiblock. Postoperative dysrhythmia requiring treatment was found in 7 patients (6%). Of 82 patients thoroughly examined by echocardiography, 37 (45%) had pulmonary regurgitation, 29 (35%) pulmonary plus tricuspid regurgitation, and 3 (4%) isolated tricuspid regurgitation. 83% of the patients had impaired lung function.

摘要

在1978年至1983年的5年期间,对114例年龄在2至24岁(平均8.4岁)的法洛四联症患者进行了矫正手术。其中41例(35.9%)此前接受过姑息手术。48例患者(42.1%)需要植入跨环补片。11名儿童在术后早期死亡(早期死亡率9.6%);后期无死亡病例。103名幸存者在术后接受了5个月至5年(平均2.4年)的随访。91例患者情况良好(88.7%),11例良好(10.7%),1例较差。9例患者(8.7%)存在残余室间隔缺损。术后心电图显示71例患者(59%)有完全性右束支传导阻滞,18例(18%)有不完全性阻滞,5例患者(5%)有完全性右束支传导阻滞伴左前分支阻滞。7例患者(6%)出现需要治疗的术后心律失常。在82例接受超声心动图全面检查的患者中,37例(45%)有肺动脉反流,29例(35%)有肺动脉加三尖瓣反流,3例(4%)有孤立性三尖瓣反流。83%的患者肺功能受损。

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