Kundal Vijay Kumar, Divya Gali, Sudhanshu Akshat, Debnath Pinaki Ranjan
Department of Pediatric Surgery, All India Institute of Medical Sciences, Jammu, Jammu and Kashmir, India.
Department of Pediatric Surgery, All India Institute of Medical Sciences, New Delhi, India.
J Indian Assoc Pediatr Surg. 2025 Sep-Oct;30(5):660-663. doi: 10.4103/jiaps.jiaps_42_25. Epub 2025 May 5.
The author reports a rare case of umbilical cord hernia with the accessory lobe of the liver entrapped in the amniotic sac with radial limb anomaly with malrotation. The accessory lobe of the liver is a rare anatomical variant of the liver that is often asymptomatic. The accessory lobe of the liver causing nonclosure of the umbilical ring is also very rare. The accessory lobe of the liver was formed during the development of embryonic body wall folds and disturbed the complete closure of the umbilical ring. If a clear-cut diagnosis of the accessory lobe is made, then it should be resected. In case of doubt, it should be fixed to the abdominal wall and regularly followed to look for signs and symptoms of torsion of the accessory lobe of the liver.
作者报告了一例罕见的脐疝病例，肝脏副叶被困于羊膜囊内，伴有桡骨肢体异常和旋转不良。肝脏副叶是一种罕见的肝脏解剖变异，通常无症状。由肝脏副叶导致脐环未闭合的情况也非常罕见。肝脏副叶是在胚胎体壁褶皱发育过程中形成的，干扰了脐环的完全闭合。如果明确诊断出肝脏副叶，应将其切除。如有疑问，应将其固定于腹壁，并定期随访，以寻找肝脏副叶扭转的体征和症状。
