Oh K S, Strife J L, Fischer K C, Teele R
AJR Am J Roentgenol. 1977 Jun;128(6):957-60. doi: 10.2214/ajr.128.6.957.
While congenital malformed and malpositioned livers are rare, they are relatively common in patients with omphaloceles. A malpositioned, malformed liver causing pyloroduodenal deformity and apparent pyloric obstruction in an infant or child with an omphalocele has not been previously reported. Thee such cases are described in which symptoms of upper gastrointestinal obstruction developed shortly after primary closure of the omphaloceles. Recognition of this condition at the time of primary closure of an omphalocele may allow consideration of additional procedures to prevent postoperative pyloric obstruction.
虽然先天性肝脏畸形和位置异常较为罕见，但在患有脐膨出的患者中相对常见。之前尚未有关于脐膨出患儿因肝脏位置异常、畸形导致幽门十二指肠畸形及明显幽门梗阻的报道。本文描述了3例这样的病例，这些病例在脐膨出一期闭合后不久出现上消化道梗阻症状。在脐膨出一期闭合时认识到这种情况，可能有助于考虑采取额外的手术措施以预防术后幽门梗阻。
