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Congenital, sporadic dysgammaglobulinaemia (absence of IgA and partial deficit in IgG and IgM).

作者信息

Scuro L A, Todesco S, Previato G, Pernis B

出版信息

Postgrad Med J. 1969 Sep;45(527):637-41. doi: 10.1136/pgmj.45.527.637.

DOI:10.1136/pgmj.45.527.637
PMID:4185634
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC2466127/
Abstract
摘要
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3113/2466127/d26715304941/postmedj00369-0067-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3113/2466127/99696173af0e/postmedj00369-0066-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3113/2466127/6bc2fa112d5b/postmedj00369-0066-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3113/2466127/6d2b773635ae/postmedj00369-0067-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3113/2466127/d26715304941/postmedj00369-0067-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3113/2466127/99696173af0e/postmedj00369-0066-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3113/2466127/6bc2fa112d5b/postmedj00369-0066-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3113/2466127/6d2b773635ae/postmedj00369-0067-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3113/2466127/d26715304941/postmedj00369-0067-b.jpg

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1
Congenital, sporadic dysgammaglobulinaemia (absence of IgA and partial deficit in IgG and IgM).先天性散发性免疫球蛋白血症(IgA缺乏,IgG和IgM部分缺乏)。
Postgrad Med J. 1969 Sep;45(527):637-41. doi: 10.1136/pgmj.45.527.637.
2
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Pract Otorhinolaryngol (Basel). 1968;30(6):353-64. doi: 10.1159/000274862.
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Correlation between gamma globulin levels and immunoglobulin IgG, IgA and IgM concentrations in blood serum.
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Content of IgG, IgA and IgM immunoglobulins in international units in normal and IgA-enriched gammaglobulins.正常及富含IgA的丙种球蛋白中IgG、IgA和IgM免疫球蛋白的国际单位含量。
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引用本文的文献

1
Recurrent haemophilus septicaemia and immunoglobulin deficiency.复发性嗜血杆菌败血症与免疫球蛋白缺乏症。
Arch Dis Child. 1970 Aug;45(242):582-4. doi: 10.1136/adc.45.242.582.

本文引用的文献

1
AN ANTIBODY DEFICIENCY SYNDROME. SELECTIVE IMMUNOGLOBULIN DEFICIENCY WITH REDUCED SYNTHESIS OF GAMMA AND ALPHA IMMUNOGLOBULIN POLYPEPTIDE CHAINS.一种抗体缺陷综合征。选择性免疫球蛋白缺乏伴γ和α免疫球蛋白多肽链合成减少。
Am J Med. 1965 Aug;39:319-34. doi: 10.1016/0002-9343(65)90058-6.
2
[IDIOPATHIC MAJOR AGAMMAGLOBULINEMIA WITH EXTENSIVE SPLENOMEGALY AND MEDIASTINAL ADENOPATHIES IN A BRONCHIECTASIC ADULT].
Presse Med (1893). 1965 Jan 27;73:241-6.
3
[DISSOCIATED ANTIBODY DEFICIENCIES. APROPOS OF A CASE OF REPEATED INFECTIONS DUE TO THE ABSCENCE OF BETA-2M AND BETA-2A GLOBULINS].[解离性抗体缺陷。关于一例因缺乏β2M和β2A球蛋白导致反复感染的病例]
Pediatrie. 1964 Mar;19:189-200.
4
BETA-2A AGLOBULINEMIA IN TWO HEALTHY MEN.两名健康男性的β-2A球蛋白血症
J Lab Clin Med. 1964 Feb;63:205-12.
5
ACQUIRED DYSGAMMAGLOBULINEMIA: ELEVATION OF THE 19S GAMMA GLOBULIN AND DEFICIENCY OF THE 7S GAMMA GLOBULIN IN A WOMAN WITH CHRONIC PROGRESSIVE BRONCHIECTASIS.
N Engl J Med. 1963 Dec 19;269:1336-40. doi: 10.1056/NEJM196312192692502.
6
Disturbances in gamma globulin synthesis as experiments of nature.作为自然实验的γ球蛋白合成紊乱
Pediatrics. 1956 Jul;18(1):109-49.
7
[Malabsorption syndrome and funicular myelosis in a patient with absence of gamma-A and gamma-M immunoglobulins in the blood].[一名血液中缺乏γ-A和γ-M免疫球蛋白的患者出现吸收不良综合征和脊髓束性软化症]
Policlinico Prat. 1966 Dec 19;73(51):1701-13.
8
[Agammaglobulinemia and its respiratory manifestations].[无丙种球蛋白血症及其呼吸系统表现]
Presse Med (1893). 1966 Nov 5;74(47):2411-6.
9
[Study of 5 cases of agammaglobulinemia with bronchopulmonary manifestations].[5例伴有支气管肺部表现的无丙种球蛋白血症的研究]
J Fr Med Chir Thorac. 1966 Feb-Mar;20(2):177-90.
10
[Agammaglobulinemia in adults and its pulmonary manifestations].[成人无丙种球蛋白血症及其肺部表现]
J Fr Med Chir Thorac. 1966 Feb-Mar;20(2):131-63.