Alday L E, Vega P J, Heller A
Chest. 1979 Mar;75(3):384-6. doi: 10.1378/chest.75.3.384.
Cor pulmonale and severe congestive heart failure secondary to chronic upper airway obstruction developed in a three-year-old girl with congenital ankylosis of the temporomandibular joint complicated by frequent respiratory infections. Nearly absent mouth opening, micrognathia, and mandibular retroposition with resultant glossoptosia obstructed the airway. Medical treatment followed by a tracheostomy and bilateral condylectomy relieved the obstruction allowing normal function of the temporomandibular joint. The clinical, electrocardiographic, radiologic, and hemodynamic findings returned to normal. Congenital ankylosis of the temporomandibular joint has not been previously reported as a cause of cor pulmonale secondary to upper airway obstruction.
一名患有颞下颌关节先天性强直并伴有频繁呼吸道感染的三岁女孩，继发于慢性上呼吸道梗阻，出现了肺心病和严重充血性心力衰竭。几乎无法张口、小颌畸形以及下颌后缩导致舌后坠，阻塞了气道。药物治疗后行气管切开术和双侧髁突切除术解除了梗阻，使颞下颌关节功能恢复正常。临床、心电图、放射学和血流动力学检查结果均恢复正常。颞下颌关节先天性强直此前尚未被报道为上呼吸道梗阻继发肺心病的病因。
