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Hepatic ultrastructure in the Hurler syndrome.

作者信息

Callahan W P, Lorincz A E

出版信息

Am J Pathol. 1966 Feb;48(2):277-98.

PMID:4221940
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC1916422/
Abstract
摘要
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/930ccb826b2c/amjpathol00279-0103-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/dea22a5290d6/amjpathol00279-0092-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/857c695fdd48/amjpathol00279-0092-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/e9a12def71c9/amjpathol00279-0094-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/8d3d257e1a37/amjpathol00279-0094-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/046e8bd16634/amjpathol00279-0096-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/cebca87fc6c0/amjpathol00279-0098-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/6bcc45e5ba27/amjpathol00279-0100-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/8bb8dc979f05/amjpathol00279-0102-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/930ccb826b2c/amjpathol00279-0103-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/dea22a5290d6/amjpathol00279-0092-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/857c695fdd48/amjpathol00279-0092-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/e9a12def71c9/amjpathol00279-0094-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/8d3d257e1a37/amjpathol00279-0094-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/046e8bd16634/amjpathol00279-0096-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/cebca87fc6c0/amjpathol00279-0098-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/6bcc45e5ba27/amjpathol00279-0100-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/8bb8dc979f05/amjpathol00279-0102-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/97ae/1916422/930ccb826b2c/amjpathol00279-0103-a.jpg

相似文献

1
Hepatic ultrastructure in the Hurler syndrome.黏多糖贮积症Ⅰ型中的肝脏超微结构。
Am J Pathol. 1966 Feb;48(2):277-98.
2
Ultrastructure of cartilage in the Hurler and Sanfilippo syndromes.黏多糖贮积症Ⅰ型和Ⅲ型中软骨的超微结构
Arch Pathol. 1972 Dec;94(6):500-10.
3
Conjunctival ultrastructure in mucolipidosis 3 (pseudo-Hurler polydystrophy).黏脂贮积症Ⅲ型(假性胡尔勒多发性营养不良)的结膜超微结构
Invest Ophthalmol. 1971 Aug;10(8):568-80.
4
Hepatic ultrastructure in mucolipidosis I (lipomucopolysaccharidosis).黏脂贮积症 I 型(脂黏多糖贮积症)中的肝脏超微结构。
Virchows Arch B Cell Pathol. 1971;7(2):189-204. doi: 10.1007/BF02892091.
5
[Clinical picture, histological and electron microscopy ophthalmic findings in an infant with Pfaundler-Hurler mucopolysaccharidosis].[一名患有范德胡勒粘多糖贮积症婴儿的临床表现、组织学及电子显微镜眼部检查结果]
Klin Monbl Augenheilkd. 1971 Oct;159(4):444-56.
6
[Histochemical and ultrastructural aspects of the liver in Hurler's disease].
Riv Anat Patol Oncol. 1966 Nov-Dec;30(5):535-47.
7
Ultrastructural studies of the skin in Hurler's syndrome.黏多糖贮积症I型皮肤的超微结构研究。
Arch Pathol. 1969 Oct;88(4):350-8.
8
Mitochondrial budding and morphogenesis of cytoplasmic vacuoles in hepatocytes of children with the Hurler syndrome and Sanfilippo disease.胡尔勒综合征和桑菲利普病患儿肝细胞中线粒体出芽及细胞质空泡的形态发生
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Mucolipidosis 3 (pseudo-Hurler polydystrophy): cytological and ultrastructural observations of cultured fibroblast cells.粘脂贮积症Ⅲ型(假性胡尔勒氏多营养不良症):培养成纤维细胞的细胞学和超微结构观察
Clin Genet. 1973;4(5):388-97. doi: 10.1111/j.1399-0004.1973.tb01165.x.
10
[Ultrastructural observation on the cornea of Hurler syndrome].[黏多糖贮积症Ⅰ型角膜的超微结构观察]
Nippon Ganka Gakkai Zasshi. 1970 Jan 10;74(1):47-56.

引用本文的文献

1
The pathology of the feline model of mucopolysaccharidosis I.猫黏多糖贮积症 I 型模型的病理学
Am J Pathol. 1983 Jul;112(1):27-36.
2
Morphologic and biochemical studies of canine mucopolysaccharidosis I.犬黏多糖贮积症I型的形态学与生物化学研究。
Am J Pathol. 1984 Mar;114(3):487-95.
3
Early prenatal diagnosis of Hurler's syndrome with termination of pregnancy and confirmatory findings on the fetus.通过终止妊娠对黏多糖贮积症I型进行早期产前诊断及胎儿的确证性检查结果。

本文引用的文献

1
TISSUE STORAGE OF MUCOPOLYSACCHARIDES IN HURLER-PFAUNDLER'S DISEASE.黏多糖在胡勒-普凡德勒病中的组织储存
Proc Natl Acad Sci U S A. 1957 Sep 15;43(9):783-90. doi: 10.1073/pnas.43.9.783.
2
OCCURRENCE OF URINARY ACID MUCOPOLYSACCHARIDES IN THE HURLER SYNDROME.黏多糖贮积症Ⅰ型中尿酸性黏多糖的出现情况。
Proc Natl Acad Sci U S A. 1957 Jun 15;43(6):443-6. doi: 10.1073/pnas.43.6.443.
3
Gargoylism; a mucopolysaccharidosis.承雷氏病;一种黏多糖贮积症。
J Med Genet. 1973 Jun;10(2):144-53. doi: 10.1136/jmg.10.2.144.
4
[The heparitinsulfate mucopolysaccharidosis (Sanfilippo). Clinical, biochemical, genetic and morphological studies].[硫酸乙酰肝素黏多糖贮积症(桑菲利波综合征)。临床、生化、遗传及形态学研究]
Klin Wochenschr. 1967 May 15;45(10):497-504. doi: 10.1007/BF01716364.
5
Aspartylglycosaminuria: a generalized storage disease. Morphological and histochemical studies.天冬氨酰氨基葡糖苷尿症:一种全身性贮积病。形态学和组织化学研究。
Acta Neuropathol. 1975;31(3):243-55. doi: 10.1007/BF00684563.
6
Coronary intimal sclerosis in Morquio's syndrome.黏多糖贮积症Ⅳ型中的冠状动脉内膜硬化
Virchows Arch A Pathol Anat Histol. 1978 Aug 4;379(1):1-10. doi: 10.1007/BF00432778.
7
The mucopolysaccharidoses.黏多糖贮积症
J Med Genet. 1976 Jun;13(3):169-81. doi: 10.1136/jmg.13.3.169.
8
Cytochemistry of the skin of patients with mucopolysaccharidoses.黏多糖贮积症患者皮肤的细胞化学
Histochem J. 1978 Mar;10(2):137-50. doi: 10.1007/BF01003299.
Scand J Clin Lab Invest. 1952;4(1):43-6. doi: 10.3109/00365515209060631.
4
Hepatocellular changes in Wilson's disease. Histochemical and electron microscopic studies.威尔逊氏病的肝细胞变化。组织化学和电子显微镜研究。
Am J Pathol. 1962 Sep;41(3):315-28.
5
Histochemical and electron microscopic study in a case of Hurler's disease.黏多糖贮积症Ⅰ型一例的组织化学与电子显微镜研究
Am J Pathol. 1962 Sep;41(3):273-86.
6
A demonstration of the structure and disposition of ferritin in the human liver cell.人肝细胞中铁蛋白的结构与分布展示。
J Ultrastruct Res. 1960 Feb;3:313-9. doi: 10.1016/s0022-5320(60)80017-2.
7
Staining methods for osmium-methacrylate sections.锇-甲基丙烯酸酯切片的染色方法。
Am J Pathol. 1959 Sep-Oct;35(5):991-7.
8
A CHARACTERISTIC BONE MARROW FINDING IN THE HURLER SYNDROME.黏多糖贮积症Ⅰ型的特征性骨髓表现。
Pediatrics. 1964 Aug;34:280-2.
9
THE USE OF VANADIUM AS A STAIN FOR ELECTRON MICROSCOPY.钒作为电子显微镜染色剂的应用。
J Cell Biol. 1964 Feb;20(2):350-6. doi: 10.1083/jcb.20.2.350.
10
The localization of acid phosphatase in rat liver cells as revealed by combined cytochemical staining and electron microscopy.通过细胞化学染色和电子显微镜联合技术揭示大鼠肝细胞中酸性磷酸酶的定位。
J Biophys Biochem Cytol. 1961 Oct;11(1):47-66. doi: 10.1083/jcb.11.1.47.