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完全性肺静脉异位引流伴房间隔完整及相关二尖瓣狭窄。

Total anomalous pulmonary venous return with intact atrial septum and associated mitral stenosis.

作者信息

Wolfe W G, Ebert P A

出版信息

Thorax. 1970 Nov;25(6):769-72. doi: 10.1136/thx.25.6.769.

DOI:10.1136/thx.25.6.769
PMID:4250293
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC472224/
Abstract

Total anomalous pulmonary venous return with an intact atrial septum is an uncommon lesion. With associated mitral stenosis each lung has a different pulmonary flow, individual vascular resistance, and function. This represents the first reported case of this anomaly treated by total correction and mitral valve replacement. Pulmonary flow reverted to normal distribution and heart size decreased, with a reversion of vascular changes on the chest radiograph one year after operation.

摘要

房间隔完整的完全性肺静脉异位引流是一种罕见的病变。合并二尖瓣狭窄时,每侧肺的肺血流量、个体血管阻力及功能均不同。本文报道了首例采用完全矫正术及二尖瓣置换术治疗该畸形的病例。术后一年,肺血流恢复正常分布,心脏大小减小,胸部X线片上血管改变也恢复正常。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9469/472224/375ebb2c1e0d/thorax00114-0129-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9469/472224/b8f3b21aa06c/thorax00114-0128-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9469/472224/375ebb2c1e0d/thorax00114-0129-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9469/472224/b8f3b21aa06c/thorax00114-0128-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9469/472224/375ebb2c1e0d/thorax00114-0129-a.jpg

相似文献

1
Total anomalous pulmonary venous return with intact atrial septum and associated mitral stenosis.完全性肺静脉异位引流伴房间隔完整及相关二尖瓣狭窄。
Thorax. 1970 Nov;25(6):769-72. doi: 10.1136/thx.25.6.769.
2
Mitral stenosis associated with partial anomalous pulmonary venous return (with intact atrial septum). An unsolved question.二尖瓣狭窄合并部分性肺静脉异位回流(房间隔完整)。一个尚未解决的问题。
Am J Cardiol. 1971 Aug;28(2):226-31. doi: 10.1016/0002-9149(71)90374-2.
3
[Partial anomalous pulmonary venous return associated with mitral stenosis].
Kyobu Geka. 1981;34(12):974-7.
4
Regional differences in pulmonary vascular resistance in the same patient. A study of partial anomalous pulmonary venous return, intact atrial septum, and mitral stenosis before and after surgical correction.
Ann Intern Med. 1980 Sep;93(3):437-40. doi: 10.7326/0003-4819-93-3-437.
5
Partial anomalous pulmonary venous connection with intact atrial septum and mitral stenosis. An evaluation.房间隔完整合并二尖瓣狭窄的部分性肺静脉异位连接。一项评估。
Indian Heart J. 1976 Jul;28(3):145-51.
6
Surgical correction of partial anomalous venous drainage with intact atrial septum: association with acquired valve lesions.
J Cardiovasc Surg (Torino). 1973 Jul-Aug;14(4):357-64.
7
Exercising pulmonary blood flow in mitral stenosis with anomalous pulmonary venous connection.二尖瓣狭窄合并肺静脉异常连接时的肺循环血流量
Chest. 1977 Mar;71(3):400-3. doi: 10.1378/chest.71.3.400.
8
Safety valve function in partial anomalous pulmonary venous drainage with mitral stenosis.二尖瓣狭窄合并部分性肺静脉异位引流时的安全阀功能
Arch Intern Med. 1972 Dec;130(6):931-4.
9
[Successful management of partial anomalous pulmonary venous drainage associated with mitral valve stenosis but without atrial septal defect].[二尖瓣狭窄合并部分性肺静脉异位引流但无房间隔缺损的成功管理]
Kyobu Geka. 1976 Aug 1;29(8):582-5.
10
Partial anomalous pulmonary venous drainage, intact atrial septum and acquired mitral stenosis. Surgical correction.
Minn Med. 1974 Jun;57(6):459-63 p.

本文引用的文献

1
Total unilateral anomalous pulmonary venous connection with intact atrial septum. Diagnostic features and a method of surgical correction.完全性单侧肺静脉异位连接伴房间隔完整。诊断特征及手术矫正方法。
Am J Cardiol. 1962 Jun;9:933-7. doi: 10.1016/0002-9149(62)90223-0.
2
PARTIAL ANOMALOUS PULMONARY VENOUS DRAINAGE WITH INTACT INTERATRIAL SEPTUM ASSOCIATED WITH CONGENITAL MITRAL STENOSIS.
Circulation. 1965 Apr;31:579-84. doi: 10.1161/01.cir.31.4.579.
3
PARTIAL ANOMALOUS PULMONARY VENOUS RETURN WITH REFERENCE TO DRAINAGE INTO THE INFERIOR VENA CAVA AND TO AN INTACT ATRIAL SEPTUM.部分性肺静脉异位回流(涉及下腔静脉引流及房间隔完整)
J Cardiovasc Surg (Torino). 1964 Jul-Aug;5:271-8.
4
MITRAL ATRESIA ASSOCIATED WITH PULMONARY VENOUS ANOMALIES.二尖瓣闭锁合并肺静脉异常
Br Heart J. 1964 Mar;26(2):241-9. doi: 10.1136/hrt.26.2.241.
5
ANOMALOUS PULMONARY VENOUS DRAINAGE ASSOCIATED WITH MITRAL STENOSIS. REPORT OF A CASE SUCCESSFULLY REPAIRED.
N Engl J Med. 1964 Jan 23;270:166-72. doi: 10.1056/NEJM196401232700402.
6
The surgical treatment of partial and total anomalous pulmonary venous connections.部分性和完全性肺静脉异位连接的外科治疗
Ann Surg. 1958 Aug;148(2):249-58. doi: 10.1097/00000658-195808000-00014.
7
Partial anomalous venous drainage.部分性肺静脉异位引流
Am J Surg. 1957 Nov;94(5):688-94. doi: 10.1016/0002-9610(57)90851-6.
8
Rheumatic mitral stenosis in association with parital anomalous pulmonary venous return.风湿性二尖瓣狭窄合并部分性肺静脉异位回流。
Thorax. 1968 Mar;23(2):197-9. doi: 10.1136/thx.23.2.197.