Marcelletti C, Wagenvoort C A, Losekoot T G, Becker A E
J Thorac Cardiovasc Surg. 1979 May;77(5):677-81.
A case history is reported of a patient with complete transposition of the great arteries and a ventricular septal defect in whom pulmonary hypertension developed, with a pulmonary resistence of 10 units M.2. Because of the possibility that the pulmonary vascular obstructive disease might have been of recent onset and that a high hematocrit value of 82 percent may have interfered with the precise determination of pulmonary resistance, an open lung biopsy was performed. The histologic findings suggested that the vascular disease was as yet reversible. Because of these findings and the aforementioned considerations, a Rastelli operation was performed instead of a palliative Mustard procedure. At present, 6 months postoperatively, the patient is asymptomatic.
报道了一例患有大动脉完全转位和室间隔缺损且出现肺动脉高压(肺阻力为10单位M.2)的患者病例。鉴于肺血管阻塞性疾病可能是近期发病,且82%的高血细胞比容值可能干扰了肺阻力的精确测定,遂进行了开胸肺活检。组织学检查结果提示血管疾病尚未出现不可逆病变。基于这些发现及上述考虑因素,实施了Rastelli手术而非姑息性的Mustard手术。目前,术后6个月,患者无症状。