Fishman R S, Bartholomew L G
Mayo Clin Proc. 1979 May;54(5):329-31.
Von Hippel-Lindau disease is a hereditary neoplastic disorder that is most commonly manifested as vascular tumors of the retina and cerebellum. Although visceral involvement is uncommon and is almost always clinically silent, we have encountered three closely related patients with extensive symptomatic pancreatic involvement. One patient had pronounced exocrine pancreatic insufficiency.
冯·希佩尔-林道病是一种遗传性肿瘤疾病，最常见的表现为视网膜和小脑的血管肿瘤。虽然内脏受累并不常见，且几乎总是临床上无症状，但我们遇到了三名密切相关的患者，他们有广泛的有症状的胰腺受累。一名患者有明显的胰腺外分泌功能不全。
