关于某些异常人类婴儿体内糖原的结构与代谢的研究。
Studies on the structure and metabolism of glycogen in some abnormal human infants.
作者信息
Manners D J, Schutt W H, Stark J R, Thambyrajah V
出版信息
Biochem J. 1971 Sep;124(3):461-5. doi: 10.1042/bj1240461.
Abstract
- The liver and muscle tissues of 14 human anencephalic babies were examined for glycogen content and structure, and for the activities of several glycogen-metabolizing enzymes. 2. In both tissues glycogen content increased with gestation age; the muscle glycogens had a slightly but significantly lower degree of branching than the corresponding liver glycogens. 3. All the expected glycogen-metabolizing enzymes were present; acid maltase activities were higher and phosphoglucomutase activities were lower than the results reported for human adult tissues. Glucose 6-phosphatase activity increased significantly with gestation age.
摘要
- 对14例人类无脑儿的肝脏和肌肉组织进行了糖原含量与结构以及几种糖原代谢酶活性的检测。2. 在这两种组织中，糖原含量均随胎龄增加；肌肉糖原的分支程度略低于相应的肝脏糖原，但差异具有统计学意义。3. 所有预期的糖原代谢酶均存在；酸性麦芽糖酶活性较高，磷酸葡萄糖变位酶活性低于报道的成人组织检测结果。葡萄糖6磷酸酶活性随胎龄显著增加。
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Studies on the structure and metabolism of glycogen in some abnormal human infants.关于某些异常人类婴儿体内糖原的结构与代谢的研究。
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