1-磷酸果糖、α-甘油磷酸和1,6-二磷酸果糖对磷酸化酶a的抑制作用：对遗传性果糖不耐受和1,6-二磷酸果糖酶缺乏症中果糖诱导的低血糖的解释。 - Suppr

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Inhibition of phosphorylase-a by fructose-1-phosphate, alpha-glycerophosphate and fructose-1,6-diphosphate: explanation for fructose-induced hypoglycaemia in hereditary fructose intolerance and fructose-1,6-diphosphatase deficiency.

作者信息

Kaufmann U, Froesch E R

出版信息

Eur J Clin Invest. 1973 Sep;3(5):407-13. doi: 10.1111/j.1365-2362.1973.tb02208.x.

DOI:10.1111/j.1365-2362.1973.tb02208.x

PMID:4359036

Abstract

摘要

相似文献

Inhibition of phosphorylase-a by fructose-1-phosphate, alpha-glycerophosphate and fructose-1,6-diphosphate: explanation for fructose-induced hypoglycaemia in hereditary fructose intolerance and fructose-1,6-diphosphatase deficiency.1-磷酸果糖、α-甘油磷酸和1,6-二磷酸果糖对磷酸化酶a的抑制作用：对遗传性果糖不耐受和1,6-二磷酸果糖酶缺乏症中果糖诱导的低血糖的解释。

Eur J Clin Invest. 1973 Sep;3(5):407-13. doi: 10.1111/j.1365-2362.1973.tb02208.x.

Decrease and inhibition of liver glycogen phosphorylase after fructose. An experimental model for the study of hereditary fructose intolerance.果糖摄入后肝糖原磷酸化酶的减少与抑制。遗传性果糖不耐受研究的实验模型。

Diabetes. 1974 Jul;23(7):597-604. doi: 10.2337/diab.23.7.597.

FRUCTOSE 1, 6-DIPHOSPHATASE IN STRIATED MUSCLE.横纹肌中的果糖1,6 - 二磷酸酶

Biochem J. 1965 Feb;94(2):436-45. doi: 10.1042/bj0940436.

Inhibition of phosphofructokinase by fructose 1,6-diphosphatase in mammalian systems: protein-protein interaction or fructose 1,6-diphosphate trapping?

Arch Biochem Biophys. 1977 Aug;182(2):563-72. doi: 10.1016/0003-9861(77)90538-0.

[Gycogenolysis disorders in the hereditary intolerance to fructose. Study of 2 cases in children].

Arch Fr Pediatr. 1973 Dec;30(10):1051-62.

On the biochemical basis of hereditary fructose intolerance.关于遗传性果糖不耐受的生化基础。

Biochem Biophys Res Commun. 1975 May 5;64(1):289-94. doi: 10.1016/0006-291x(75)90251-x.

High liver glycogen in hereditary fructose intolerance.遗传性果糖不耐受症中的高肝糖原

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Effect of fructose 1-phosphate on the activation of liver glycogen synthase.1-磷酸果糖对肝糖原合酶激活的影响。

Biochem J. 1985 Nov 15;232(1):133-7. doi: 10.1042/bj2320133.

[Fructose 1,6-diphosphatase deficiency in 2 sisters].[两姐妹患1,6-二磷酸果糖酶缺乏症]

Arch Fr Pediatr. 1975 Feb;32(2):113-21.

Hepatic fructose-1,6-diphosphatase deficiency. A cause of lactic acidosis and hypoglycemia in infancy.肝果糖-1,6-二磷酸酶缺乏症。婴儿期乳酸酸中毒和低血糖的一个病因。

J Clin Invest. 1972 Aug;51(8):2115-23. doi: 10.1172/JCI107018.

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Hereditary fructose intolerance.遗传性果糖不耐受症

J Med Genet. 1998 May;35(5):353-65. doi: 10.1136/jmg.35.5.353.

A possible case of transient hereditary fructose intolerance.一例可能的短暂性遗传性果糖不耐受病例。

J Inherit Metab Dis. 1993;16(1):73-7. doi: 10.1007/BF00711318.

The catalytic activity of phosphorylase b in the liver. With a note on the assay in the glycogenolytic direction.肝脏中磷酸化酶b的催化活性。附带关于糖原分解方向测定的说明。

Biochem J. 1981 Nov 15;200(2):327-36. doi: 10.1042/bj2000327.

Effect of fructose 1-phosphate on the activation of liver glycogen synthase.1-磷酸果糖对肝糖原合酶激活的影响。

Biochem J. 1985 Nov 15;232(1):133-7. doi: 10.1042/bj2320133.

Simultaneous synthesis and degradation of rat liver glycogen. An in vivo nuclear magnetic resonance spectroscopic study.大鼠肝脏糖原的同步合成与降解。一项体内核磁共振波谱研究。

J Clin Invest. 1990 Aug;86(2):612-7. doi: 10.1172/JCI114752.

Effects of lactate on pathways of glycogen formation in the perfused rat liver.乳酸对灌注大鼠肝脏中糖原形成途径的影响。

Biochem J. 1991 Dec 1;280 ( Pt 2)(Pt 2):415-9. doi: 10.1042/bj2800415.

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