[Gycogenolysis disorders in the hereditary intolerance to fructose. Study of 2 cases in children]. - Suppr | 超能文献

[Gycogenolysis disorders in the hereditary intolerance to fructose. Study of 2 cases in children].

作者信息

Rambaud P, Joannard A, Bost M, Marchal A, Rachail M, Roget J

出版信息

Arch Fr Pediatr. 1973 Dec;30(10):1051-62.

Abstract

摘要

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[Gycogenolysis disorders in the hereditary intolerance to fructose. Study of 2 cases in children].

Arch Fr Pediatr. 1973 Dec;30(10):1051-62.

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[Hereditary fructose intolerance (author's transl)].遗传性果糖不耐受症（作者译）

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The glycogenoses and other inherited disorders of carbohydrate metabolism.糖原贮积病及其他遗传性碳水化合物代谢紊乱疾病。

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Inhibition of phosphorylase-a by fructose-1-phosphate, alpha-glycerophosphate and fructose-1,6-diphosphate: explanation for fructose-induced hypoglycaemia in hereditary fructose intolerance and fructose-1,6-diphosphatase deficiency.1-磷酸果糖、α-甘油磷酸和1,6-二磷酸果糖对磷酸化酶a的抑制作用：对遗传性果糖不耐受和1,6-二磷酸果糖酶缺乏症中果糖诱导的低血糖的解释。

Eur J Clin Invest. 1973 Sep;3(5):407-13. doi: 10.1111/j.1365-2362.1973.tb02208.x.

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[Fructose 1,6-diphosphatase deficiency in 2 sisters].[两姐妹患1,6-二磷酸果糖酶缺乏症]

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[Study of blood glucose, lactate and insulin responses after rapid intravenous administration of variable doses of fructose in normal children].[正常儿童静脉快速注射不同剂量果糖后血糖、乳酸和胰岛素反应的研究]

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引用本文的文献

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Molecular aspects of fructose metabolism and metabolic disease.果糖代谢与代谢性疾病的分子基础

Cell Metab. 2021 Dec 7;33(12):2329-2354. doi: 10.1016/j.cmet.2021.09.010. Epub 2021 Oct 6.

2

Evidence that the severity of depletion of inorganic phosphate determines the severity of the disturbance of adenine nucleotide metabolism in the liver and renal cortex of the fructose-loaded rat.无机磷酸盐耗竭的严重程度决定果糖负荷大鼠肝脏和肾皮质中腺嘌呤核苷酸代谢紊乱严重程度的证据。

J Clin Invest. 1978 Jan;61(1):209-20. doi: 10.1172/JCI108920.