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对梅干腹综合征进行最小限度的手术干预。

Minimal surgical interference in the prune belly syndrome.

作者信息

Woodhouse C R, Kellett M J, Williams D I

出版信息

Br J Urol. 1979 Dec;51(6):475-80. doi: 10.1111/j.1464-410x.1979.tb03582.x.

DOI:10.1111/j.1464-410x.1979.tb03582.x
PMID:43757
Abstract

Twenty-seven cases of prune belly syndrome which were well in the neonatal period are reported. Eleven were seen in the first year of life and 16 presented later. The first line of treatment was to ensure proper bladder emptying, usually by urethrotomy. Thereafter a policy of minimal surgical interference was followed, operating only for proven obstruction and intractable infection. This policy appears justified as 10 of 11 early presenters have done well. In the late presenters it was accepted that some renal damage had already occurred; nonetheless, 11 of 16 cases have done well. The X-rays were reviewed and hitherto unreported medullary cysts were noted. No radiological signs were found that were of prognostic significance.

摘要

报告了27例在新生儿期情况良好的梅干腹综合征病例。11例在出生后第一年内出现,16例较晚出现。首要治疗措施是确保膀胱充分排空,通常通过尿道切开术。此后遵循尽量减少手术干预的策略,仅对已证实的梗阻和难以控制的感染进行手术。这一策略似乎是合理的,因为11例早期出现症状的患者中有10例情况良好。对于较晚出现症状的患者,人们认为已经发生了一些肾损害;尽管如此,16例中有11例情况良好。对X线片进行了复查,发现了此前未报告的髓质囊肿。未发现具有预后意义的放射学征象。

相似文献

1
Minimal surgical interference in the prune belly syndrome.对梅干腹综合征进行最小限度的手术干预。
Br J Urol. 1979 Dec;51(6):475-80. doi: 10.1111/j.1464-410x.1979.tb03582.x.
2
The prune belly syndrome.
Urol Clin North Am. 1978 Feb;5(1):75-93.
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The early assessment for individualized treatment in the prune belly syndrome.梅干腹综合征个体化治疗的早期评估
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Total surgical reconstruction for patients with abdominal muscular deficiency ("prune-belly") syndrome.针对腹部肌肉缺损(“梅干腹”)综合征患者的全手术重建。
J Pediatr Surg. 1977 Dec;12(6):1033-43. doi: 10.1016/0022-3468(77)90616-9.
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Prune belly syndrome in young females.年轻女性的梅干腹综合征。
Urol Radiol. 1979;1(3):151-5. doi: 10.1007/BF02926619.
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Urodynamics in the prune belly syndrome.梅干腹综合征的尿动力学检查
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Orchiopexy in the prune belly syndrome.
Br J Urol. 1978 Aug;50(5):348-51. doi: 10.1111/j.1464-410x.1978.tb03646.x.
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Resection of the urethra with the prune belly syndrome.
Birth Defects Orig Artic Ser. 1977;13(5):95-6.
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[Congenital triade of abdominal muscular deficiency, urinary tract abnormality and cryptorchidism. (Prune belly syndrome) (author's transl)].先天性腹部肌肉发育不全、尿路异常和隐睾三联征。(梅干腹综合征)(作者译)
J Urol Nephrol (Paris). 1978 Oct-Nov;84(10-11):729-30, 731-2.
10
Congenital megalourethra associated with prune belly syndrome.与梅干腹综合征相关的先天性巨尿道
J Urol. 1976 Dec;116(6):814-5. doi: 10.1016/s0022-5347(17)59027-8.

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Prune belly syndrome.梅干腹综合征
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The prune-belly syndrome: current insights.
Pediatr Nephrol. 1995 Dec;9(6):770-8. doi: 10.1007/BF00868740.
5
Prune belly syndrome--report of 47 cases.梅干腹综合征——47例报告。
Arch Dis Child. 1982 Nov;57(11):856-9. doi: 10.1136/adc.57.11.856.
6
Surgical correction and rehabilitation for children with "Prune-belly" syndrome.“梅干腹”综合征患儿的手术矫正与康复治疗
Ann Surg. 1981 Jun;193(6):757-62. doi: 10.1097/00000658-198106000-00011.