DeLozier H L, Gacek R R, Dana S T
Ann Otol Rhinol Laryngol. 1979 Mar-Apr;88(2 Pt 1):187-91. doi: 10.1177/000348947908800207.
Two cases of unsuspected intralabyrinthine schwannoma are reported and the literature is reviewed. The mean age of the patients was 56 years, with the most common symptoms being hearing loss, dizziness, and tinnitus. All patients demonstrated a profound sensorineural hearing loss with low discrimination scores, and recruitment was elicited in two patients. A radiographic evaluation was negative in all but one case. Five of the six patients had a preoperative diagnosis of Ménière's disease. Transcanal labyrinthectomy was employed to remove tumor in all patients. This review suggests that a patient, presenting with symptoms of atypical Ménière's disease and negative radiographic evaluation, should alert the surgeon to the possibility of an intralabyrinthine schwannoma.
本文报告了2例未被怀疑的迷路内神经鞘瘤病例，并对相关文献进行了综述。患者的平均年龄为56岁，最常见的症状为听力损失、头晕和耳鸣。所有患者均表现为严重的感音神经性听力损失且辨别分数较低，2例患者出现重振现象。除1例病例外，所有病例的影像学评估均为阴性。6例患者中有5例术前诊断为梅尼埃病。所有患者均采用经耳道迷路切除术切除肿瘤。本综述表明，对于表现出非典型梅尼埃病症状且影像学评估为阴性的患者，外科医生应警惕迷路内神经鞘瘤的可能性。
