Richardson R R, Siqueira E B, Oi S, Nunez C
Neurosurgery. 1979 Jan;4(1):66-70. doi: 10.1227/00006123-197901000-00014.
Two cases of solitary neurogenic tumors of the brachial plexus unassociated with von Recklinghausen's disease are presented. One patient had a malignant schwannoma. The lesion of the other patient was benign and was diagnosed pathologically as a plexiform neurofibroma. These uncommon neurogenic tumors of the brachial plexus unassociated with von Recklinghausen's disease pose diagnostic and surgical problems. The initial clinical presentation is usually that of a painless supraclavicular mass. At the time of surgical exploration, the exact site or nerve of origin cannot always be identified. If motor loss is caused by such a tumor of the brachial plexus, it usually indicates a malignant lesion and a poor prognosis. Although wide radical excision of a malignant neurogenic tumor is indicated surgically, one of our patients had an early malignant recurrence that necessitated immediate amputation.
本文报告两例与冯雷克林霍增氏病无关的臂丛神经孤立性神经源性肿瘤。一例患者患有恶性神经鞘瘤。另一例患者的病变为良性，经病理诊断为丛状神经纤维瘤。这些与冯雷克林霍增氏病无关的臂丛神经罕见神经源性肿瘤带来了诊断和手术方面的问题。最初的临床表现通常是无痛性锁骨上肿块。在手术探查时，并不总能确定确切的起源部位或神经。如果臂丛神经的此类肿瘤导致运动功能丧失，通常提示为恶性病变且预后不良。虽然手术时需要对恶性神经源性肿瘤进行广泛根治性切除，但我们的一位患者早期出现恶性复发，不得不立即截肢。
