Ikeda T, Ishihara T, Yoshimatsu H, Kikuchi K, Murakami M
Thorax. 1974 Sep;29(5):582-8. doi: 10.1136/thx.29.5.582.
. , 582-588. . A 22-year-old man with primary osteogenic sarcoma of the superior mediastinum is reported. This case is the second instance of primary osteogenic sarcoma of the mediastinum and the first case of superior mediastinal origin to be reported. The patient had local recurrence one year after the first operation. After resection of the recurrent tumour with left upper lobectomy and partial pericardectomy followed by radiation, he has been well for more than five years without recurrence. Extraosseous osteogenic sarcoma of soft tissue is very rare and has been reported in 103 patients. The five-year survival of patients with extraosseous osteogenic sarcoma is 22·4%. The distribution and prognosis of this tumour are similar to those of rhabdomyosarcoma in soft tissue. Primary amputation or wide excision is the treatment of choice.
报道了一名22岁患有纵隔原发性骨肉瘤的男性患者。该病例是纵隔原发性骨肉瘤的第二例，也是首例报道的起源于上纵隔的病例。患者在首次手术后一年出现局部复发。在切除复发性肿瘤并行左上叶切除及部分心包切除术后进行放疗，他已健康存活超过五年且无复发。软组织骨外骨肉瘤非常罕见，已有103例患者的报道。骨外骨肉瘤患者的五年生存率为22.4%。该肿瘤的分布和预后与软组织横纹肌肉瘤相似。原发性截肢或广泛切除是首选治疗方法。
