十二指肠和空肠闭锁伴背侧肠系膜发育不全：“苹果皮样”小肠。

Duodenal and jejunal atresia with agenesis of the dorsal mesentery: "apple peel" small bowel.

作者信息

Zivković S M, Milosević V R

出版信息

Am J Surg. 1979 May;137(5):676-8. doi: 10.1016/0002-9610(79)90047-3.

Abstract

Two newborn infants with duodenal and jejunal atresia and agenesis of the dorsal mesentery represent our surgical experience with "apple peel" small bowel or "christmas tree" demormity. The first patient had the typical appearance of this condition. The postoperative course was complicated by hyperbilirubinemia, septicemia, and disseminated intravascular coagulation. The infant is in satisfactory condition 1.5 years after operation. The second patient had agenesis of the dorsal mesentery without spiraling of the bowel around its vascular stalk. The child died after 1 month, with complete absence of extrahepatic bile ducts as seen at a second laparotomy. Neither child had been subjected to gastrostomy.

摘要

两名患有十二指肠和空肠闭锁以及背侧肠系膜发育不全的新生儿代表了我们对“苹果皮”样小肠或“圣诞树”样畸形的手术经验。首例患者具有该病症的典型表现。术后病程因高胆红素血症、败血症和弥散性血管内凝血而复杂化。该婴儿在术后1.5年状况良好。第二例患者存在背侧肠系膜发育不全，且肠管未围绕其血管蒂螺旋状排列。该患儿在1个月后死亡，二次剖腹探查时发现完全没有肝外胆管。两名患儿均未接受胃造口术。