Chaouat Y, Faures B, Ginet C l, Paquet J, Piatecki A
Rev Rhum Mal Osteoartic. 1974 Oct;41(10):593-9.
With reference to 27 cases reported in the literature (of which 1 was personal) of primary hypogammaglobulinaemia in adults (PHGGA) with rheumatic manifestations, and following a statistical study, the authors think that the rheumatic manifestations that precede, accompany, or follow primary hypogammaglobulinaemia in adults are not coincidental. These manifestations occur in 10 percent of patients. The clinical and radiological pictures, and the associated infections and immunological disorders form a particular clinical entity and lead to therapeutic difficultires. In this connexion, the authors mention in particular pathogenic problems related to hypogammaglobulinaemia in adults and the rheumatic manifestations.
参考文献中报道的27例（其中1例为本人病例）成人原发性低丙种球蛋白血症（PHGGA）伴有风湿表现的病例，并经过统计学研究，作者认为成人原发性低丙种球蛋白血症之前、伴随或之后出现的风湿表现并非偶然。这些表现在10%的患者中出现。临床和放射学表现，以及相关的感染和免疫紊乱构成了一种特殊的临床实体，并导致治疗困难。在这方面，作者特别提到了与成人低丙种球蛋白血症和风湿表现相关的致病问题。
