Kleinman P K
Radiology. 1979 Aug;132(2):281-4. doi: 10.1148/132.2.281.
The radiological features of absence of a pulmonary artery are often characteristic enough to allow a diagnosis based on the plain radiograph. They include a small hemithorax, ipsilateral displacement of the mediastinum, absence of the corresponding pulmonary artery, and reticular parenchymal densities, generally attributed to bronchial collateral vessels. Six cases are reported; 3 patients had peripheral, hazy, confluent densities and pleural thickening. Aortography disclosed extensive intercostal and subdiaphragmatic transpleural collaterals, which formed telangiectatic networks within the pleura of the oligemic lungs, corresponding to the areas of increased density on the plain radiographs. The appearance of these transpleural collaterals is helpful in diagnosis. Pleural telangiectasia in association with prolonged pulmonary oligemia of any cause indicates significant transpleural collaterals.
肺动脉缺如的放射学特征通常具有足够的特异性，能够在平片的基础上做出诊断。这些特征包括半侧胸廓变小、纵隔向患侧移位、相应肺动脉缺如以及网状肺实质密度增高，后者通常归因于支气管侧支血管。本文报告6例；3例患者有外周模糊的融合性密度影及胸膜增厚。主动脉造影显示广泛的肋间和膈下经胸膜侧支血管，这些血管在肺血量减少的肺脏胸膜内形成毛细血管扩张网，与平片上密度增高区域相对应。这些经胸膜侧支血管的表现有助于诊断。任何原因导致的长期肺血量减少伴胸膜毛细血管扩张提示存在明显的经胸膜侧支血管。
