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Multiple exchange transfusions as treatment during the acute period in maple syrup urine disease.

作者信息

Schuchmann L, Witt I, Schulz P, Schumacher H, Rüdiger H

出版信息

Helv Paediatr Acta. 1972 Sep;27(4):449-56.

PMID:4644280
Abstract
摘要

相似文献

1
Multiple exchange transfusions as treatment during the acute period in maple syrup urine disease.
Helv Paediatr Acta. 1972 Sep;27(4):449-56.
2
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[Metabolic study of the classic form of leucinosis during exchange transfusion therapy].
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[Neonatal diagnosis of maple syrup urine disease and trial of exchange transfusion].[枫糖尿症的新生儿诊断及换血疗法试验]
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Leucine equivalency system in managing branched chain ketoaciduria.
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引用本文的文献

1
Peritoneal dialysis in maple-syrup-urine disease: studies on branched-chain amino and keto acids.
Eur J Pediatr. 1980 Jun;134(1):57-63. doi: 10.1007/BF00442404.
2
Hudson memorial lecture. Neonatal management of organic acidurias. Clinical update.哈德逊纪念讲座。有机酸尿症的新生儿管理。临床进展
J Inherit Metab Dis. 1984;7 Suppl 1:2-9. doi: 10.1007/978-94-009-5612-4_2.
3
Organic acids and branched-chain amino acids in body fluids before and after multiple exchange transfusions in maple syrup urine disease.
J Inherit Metab Dis. 1983;6(4):183-9. doi: 10.1007/BF02310879.
4
Defective decarboxylase in branched chain ketoacid oxidase multienzyme complex in classic type of maple syrup urine disease.经典型枫糖尿症中支链酮酸氧化酶多酶复合物中的脱羧酶缺陷。
Humangenetik. 1972;14(4):257-63. doi: 10.1007/BF00290167.
5
Maple syrup urine disease: treatment of the acutely ill newborn.
Eur J Pediatr. 1978 Oct 12;129(3):157-65. doi: 10.1007/BF00442159.