Beitzke A, Anderson R H, Wilkinson J L, Shinebourne E A
Br Heart J. 1979 Jul;42(1):22-6. doi: 10.1136/hrt.42.1.22.
Two cases are described of a most unusual variant of two-chambered right ventricle. In both the ventricular septal defect was between the distal chamber of the right ventricle and the left ventricle. However the extensive dividing 'septum' between proximal and distal parts of the right ventricle converted the latter, haemodynamically, into part of the left ventricle. In the first case the distal chamber supported the aorta in the left anterior position, the pulmonary artery arising from the proximal part of the right ventricle. In the second the pulmonary artery arose from the distal chamber and the aorta from the proximal chamber. Though in both the ventriculoarterial connection was double outlet right ventricle, functionally there was arterial concordance in case 1 and discordance in case 2. A further disconcerting feature was the resemblance of the distal right ventricular chamber to the rudimentary chamber of a univentricular heart of left ventricular type.
本文描述了两例极为罕见的双腔右心室变异病例。两例患者的室间隔缺损均位于右心室远侧腔与左心室之间。然而，右心室近侧部与远侧部之间广泛的分隔“隔膜”在血流动力学上使后者转变为左心室的一部分。在第一例中，远侧腔在左前位连接主动脉，肺动脉发自右心室近侧部。在第二例中，肺动脉发自远侧腔，主动脉发自近侧腔。虽然两例的心室动脉连接均为右心室双出口，但在功能上，例1存在动脉一致性，例2存在动脉不一致性。另一个令人困惑的特征是右心室远侧腔类似于左心室型单心室心脏的发育不全腔。
