黏脂贮积症I型（唾液酸沉积症）和黏脂贮积症II型（I-细胞病）成纤维细胞的寡糖和神经节苷脂神经氨酸酶活性 - Suppr

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Oligosaccharide and ganglioside neuraminidase activities of mucolipidosis I (sialidosis) and mucolipidosis II (I-cell disease) fibroblasts.

作者信息

Cantz M, Messer H

出版信息

Eur J Biochem. 1979 Jun;97(1):113-8. doi: 10.1111/j.1432-1033.1979.tb13091.x.

DOI:10.1111/j.1432-1033.1979.tb13091.x

PMID:477659

Abstract

摘要

相似文献

Oligosaccharide and ganglioside neuraminidase activities of mucolipidosis I (sialidosis) and mucolipidosis II (I-cell disease) fibroblasts.黏脂贮积症I型（唾液酸沉积症）和黏脂贮积症II型（I-细胞病）成纤维细胞的寡糖和神经节苷脂神经氨酸酶活性

Eur J Biochem. 1979 Jun;97(1):113-8. doi: 10.1111/j.1432-1033.1979.tb13091.x.

[Studies on sialidosis and mucolipidosis. Properties of neuraminidase in cultured skin fibroblasts].[涎酸沉积症和粘脂贮积症的研究。培养皮肤成纤维细胞中神经氨酸酶的特性]

Biochim Biophys Acta. 1982 Sep 7;706(2):212-20. doi: 10.1016/0167-4838(82)90489-7.

Neuraminidase studies in sialidosis.唾液酸贮积症中的神经氨酸酶研究。

Adv Exp Med Biol. 1980;125:415-30. doi: 10.1007/978-1-4684-7844-0_38.

Mucolipidosis type IV: ganglioside sialidase deficiency.

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Catalytically defective ganglioside neuraminidase in mucolipidosis IV.黏脂贮积症IV型中催化缺陷的神经节苷脂神经氨酸酶

Clin Genet. 1982 Jun;21(6):374-81. doi: 10.1111/j.1399-0004.1982.tb01390.x.

Partial characterization and studies of fibroblast and leucocyte neuraminidase activities towards sialyloligosaccharides in adult sialidosis and mucolipidosis II and III.

Biochim Biophys Acta. 1981 Dec 15;662(2):220-5. doi: 10.1016/0005-2744(81)90033-4.

Neuraminidase activities in sialidosis and mucolipidosis.唾液酸沉积症和粘脂贮积症中的神经氨酸酶活性。

J Neurol Sci. 1982 May;54(2):181-7. doi: 10.1016/0022-510x(82)90180-0.

Ganglioside GM3 sialidase activity in fibroblasts of normal individuals and of patients with sialidosis and mucolipidosis IV. Subcellular distribution and and some properties.正常个体、唾液酸沉积症患者和黏脂贮积症IV型患者成纤维细胞中神经节苷脂GM3唾液酸酶活性。亚细胞分布及一些特性。

Biochem J. 1989 May 15;260(1):69-74. doi: 10.1042/bj2600069.

[Mucolipidosis II (I cell disease): a sialidosis?].[黏脂贮积症II型（I细胞病）：一种唾液酸沉积症？]

Arch Fr Pediatr. 1979 Mar;36(3):225-34.

Deficiency of neuraminidase in the sialidoses and the mucolipidoses.唾液酸沉积症和粘脂贮积症中神经氨酸酶的缺乏。

Hum Genet. 1980;53(3):383-8. doi: 10.1007/BF00287060.

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Cellular localization of neuraminidases in cultured human fibroblasts.神经氨酸酶在培养的人成纤维细胞中的细胞定位

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Characterization of human placental neuraminidases. Stability, substrate specificity and molecular weight.人胎盘神经氨酸酶的特性：稳定性、底物特异性及分子量

Biochem J. 1982 Aug 1;205(2):345-51. doi: 10.1042/bj2050345.

Mucolipidosis I. Roentgenographic follow-up.黏脂贮积症I型。X线随访

Skeletal Radiol. 1984;12(3):153-61. doi: 10.1007/BF00361081.

Specificity studies on the oligosaccharide neuraminidase of human fibroblasts.人成纤维细胞寡糖神经氨酸酶的特异性研究

Biochem J. 1984 Mar 1;218(2):625-8. doi: 10.1042/bj2180625.

Ganglioside GM1 metabolism in living human fibroblasts with beta-galactosidase deficiency.β-半乳糖苷酶缺乏的人活体成纤维细胞中神经节苷脂GM1的代谢

Hum Genet. 1986 May;73(1):35-8. doi: 10.1007/BF00292661.

Biochem J. 1989 May 15;260(1):69-74. doi: 10.1042/bj2600069.

Disorders of glycoprotein degradation.糖蛋白降解紊乱。

J Inherit Metab Dis. 1990;13(4):523-37. doi: 10.1007/BF01799510.

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