Pernot C
Angiology. 1979 Sep;30(9):640-4. doi: 10.1177/000331977903000908.
From the time of birth, a patient a rapidly expanding pulsatile mass in the left upper extremity. The findings are those of multiple AV fistulae: thrill, continuous murmur, cutaneous angioma, and rapidly appearing trophic changes. Cyanosis and irreversible heart failure ensued, and the patient died after 20 hours of life. An aortogram revealed numerous AV fistulas within an angiomatous network vascularized by a huge subclavian artery and drained by a large subclavian vein.
自出生起，一名患者左上肢出现一个迅速增大的搏动性肿块。检查结果显示为多发性动静脉瘘：震颤、连续性杂音、皮肤血管瘤以及迅速出现的营养性改变。随后出现了发绀和不可逆的心力衰竭，患者在出生20小时后死亡。主动脉造影显示在一个由巨大锁骨下动脉供血、经一条粗大锁骨下静脉引流的血管瘤样血管网络内有大量动静脉瘘。
