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右肺静脉闭锁及左肺静脉异常引流至门静脉循环。

Atresia of right pulmonary veins and anomalous left pulmonary venous drainage into portal circulation.

作者信息

Samánek M, Tüma S, Benesová D, Povýsilová V, Prazský F, Cápova E

出版信息

Thorax. 1974 Jul;29(4):446-50. doi: 10.1136/thx.29.4.446.

DOI:10.1136/thx.29.4.446
PMID:4850684
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC470178/
Abstract

, , 446-450. An anomaly of pulmonary venous drainage in a male newborn infant is described whereby the left pulmonary veins entered the portal vein and the right pulmonary veins were atretic. A correct diagnosis was made by detecting high-oxygen saturation in the hepatic veins, right-to-left shunt at atrial level, and increased pulmonary artery wedge pressure in comparison with the left atrial pressure, and was confirmed by angiography.

摘要

描述了一名男性新生儿的肺静脉引流异常,其中左肺静脉进入门静脉,右肺静脉闭锁。通过检测肝静脉中的高氧饱和度、心房水平的右向左分流以及与左心房压力相比肺动脉楔压升高做出了正确诊断,并通过血管造影得到证实。 (页码:446 - 450)

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ed1/470178/cc84564d6cb0/thorax00136-0072-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ed1/470178/d6367bf29037/thorax00136-0069-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ed1/470178/2c9b26dcdc82/thorax00136-0069-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ed1/470178/742ac7a4b241/thorax00136-0069-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ed1/470178/4fb51d3cffaa/thorax00136-0070-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ed1/470178/a1e5a9b67d89/thorax00136-0071-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ed1/470178/cc84564d6cb0/thorax00136-0072-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ed1/470178/d6367bf29037/thorax00136-0069-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ed1/470178/2c9b26dcdc82/thorax00136-0069-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ed1/470178/742ac7a4b241/thorax00136-0069-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ed1/470178/4fb51d3cffaa/thorax00136-0070-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ed1/470178/a1e5a9b67d89/thorax00136-0071-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/3ed1/470178/cc84564d6cb0/thorax00136-0072-a.jpg

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Atresia of right pulmonary veins and anomalous left pulmonary venous drainage into portal circulation.右肺静脉闭锁及左肺静脉异常引流至门静脉循环。
Thorax. 1974 Jul;29(4):446-50. doi: 10.1136/thx.29.4.446.
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引用本文的文献

1
Supracardiac anomalous pulmonary venous connection with unilateral pulmonary venous atresia: Diagnosis and management.心上型肺静脉异常连接合并单侧肺静脉闭锁:诊断与治疗
Ann Pediatr Cardiol. 2009 Jul;2(2):153-5. doi: 10.4103/0974-2069.58318.
2
Unilateral absence or extreme hypoplasia of pulmonary veins.肺静脉单侧缺如或极度发育不全。
Br Heart J. 1983 Feb;49(2):148-53. doi: 10.1136/hrt.49.2.148.
3
The significance of lung scintigraphy in anomalies of the pulmonary vascular bed.肺闪烁显像在肺血管床异常中的意义。

本文引用的文献

1
Atresia of the common pulmonary vein.肺总静脉闭锁
Pediatrics. 1962 May;29:729-39.
2
Regional pulmonary function studied with xenon 133.用氙133研究局部肺功能。
J Clin Invest. 1962 Mar;41(3):519-31. doi: 10.1172/JCI104505.
Pediatr Radiol. 1975 Nov 24;4(1):21-7. doi: 10.1007/BF00978815.