Cogswell J J, Risdon R A, Taylor B
Arch Dis Child. 1974 Jul;49(7):520-4. doi: 10.1136/adc.49.7.520.
Two sisters are described with fatal chronic obstructive lung disease of unknown origin. The lung condition was clinically and histologically indistinguishable from cystic fibrosis and the salivary glands showed pathological changes expected in cystic fibrosis. Neither child had abnormal sweat electrolytes, they had no bowel symptoms, and the pancreas was normal at necropsy.
本文描述了两姐妹患有病因不明的致命性慢性阻塞性肺病。肺部疾病在临床和组织学上与囊性纤维化无法区分，且唾液腺显示出囊性纤维化预期的病理变化。两个孩子的汗液电解质均无异常，没有肠道症状，尸检时胰腺正常。
