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The lipoproteins and lipid transport in abetalipoproteinemia.

作者信息

Levy R I, Fredrickson D S, Laster L

出版信息

J Clin Invest. 1966 Apr;45(4):531-41. doi: 10.1172/JCI105367.

DOI:10.1172/JCI105367
PMID:4957009
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC292727/
Abstract
摘要
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25d9/292727/b56fa3cd1d92/jcinvest00262-0159-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25d9/292727/e9508e419dfe/jcinvest00262-0155-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25d9/292727/2e2a98d42321/jcinvest00262-0155-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25d9/292727/01968b9ac689/jcinvest00262-0156-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25d9/292727/48a438bfdecd/jcinvest00262-0156-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25d9/292727/133fe93369df/jcinvest00262-0157-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25d9/292727/c6dd5b4f7cb3/jcinvest00262-0157-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25d9/292727/334b38bca87a/jcinvest00262-0157-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25d9/292727/b56fa3cd1d92/jcinvest00262-0159-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25d9/292727/e9508e419dfe/jcinvest00262-0155-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25d9/292727/2e2a98d42321/jcinvest00262-0155-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25d9/292727/01968b9ac689/jcinvest00262-0156-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25d9/292727/48a438bfdecd/jcinvest00262-0156-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25d9/292727/133fe93369df/jcinvest00262-0157-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25d9/292727/c6dd5b4f7cb3/jcinvest00262-0157-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25d9/292727/334b38bca87a/jcinvest00262-0157-c.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/25d9/292727/b56fa3cd1d92/jcinvest00262-0159-a.jpg

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The lipoproteins and lipid transport in abetalipoproteinemia.无β脂蛋白血症中的脂蛋白与脂质转运
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本文引用的文献

1
The phospholipins of blood.血液中的磷脂
Biochem J. 1935 Jul;29(7):1683-9. doi: 10.1042/bj0291683.
2
Malformation of the erythrocytes in a case of atypical retinitis pigmentosa.非典型色素性视网膜炎病例中的红细胞畸形。
Blood. 1950 Apr;5(4):381-87.
3
Acanthrocytosis; a genetic erythrocytic malformation.棘红细胞增多症;一种遗传性红细胞畸形。
J Clin Invest. 1974 Feb;53(2):440-53. doi: 10.1172/JCI107578.
4
Abnormalities of high density lipoproteins in abetalipoproteinemia.无β脂蛋白血症中高密度脂蛋白异常。
J Clin Invest. 1967 Jul;46(7):1151-61. doi: 10.1172/JCI105608.
5
Peroxidative hemolysis of red blood cells from patients with abetalipoproteinemia (acanthocytosis).无β脂蛋白血症(棘状红细胞增多症)患者红细胞的过氧化溶血
J Clin Invest. 1967 Mar;46(3):357-68. doi: 10.1172/JCI105537.
6
A comparison of heritable abnormal lipoprotein patterns as defined by two different techniques.两种不同技术所定义的遗传性异常脂蛋白模式的比较。
J Clin Invest. 1969 Nov;47(11):2446-57. doi: 10.1172/JCI105927.
7
Disturbed release of lipoprotein from ethanol-induced fatty liver.乙醇诱导的脂肪肝中脂蛋白释放紊乱。
Experientia. 1968 May 15;24(5):438-9. doi: 10.1007/BF02144375.
8
Bile salts and cholesterol in the pathogenesis of target cells in obstructive jaundice.胆汁盐和胆固醇在梗阻性黄疸靶细胞发病机制中的作用
J Clin Invest. 1968 Apr;47(4):809-22. doi: 10.1172/JCI105775.
9
The regulation of plasma lipoprotein concentrations as affected in human mutants.人类突变体中血浆脂蛋白浓度的调控。
Proc Natl Acad Sci U S A. 1969 Nov;64(3):1138-46. doi: 10.1073/pnas.64.3.1138.
10
Fat absorption during inhibition of protein synthesis: studies of lymph chylomicrons.蛋白质合成受抑制期间的脂肪吸收:淋巴乳糜微粒研究
J Clin Invest. 1972 Feb;51(2):356-63. doi: 10.1172/JCI106821.
Blood. 1952 Jun;7(6):577-91.
4
Protein measurement with the Folin phenol reagent.使用福林酚试剂进行蛋白质测定。
J Biol Chem. 1951 Nov;193(1):265-75.
5
HETEROGENEITY OF PLASMA HIGH DENSITY LIPOPROTEINS.血浆高密度脂蛋白的异质性
J Clin Invest. 1965 Mar;44(3):426-41. doi: 10.1172/JCI105156.
6
STUDIES OF THE COMPOSITION AND STRUCTURE OF SERUM LIPOPROTEINS: PHYSICAL-CHEMICAL CHARACTERIZATION OF PHOSPHOLIPID-PROTEIN RESIDUES OBTAINED FROM VERY-LOW-DENSITY HUMAN SERUM LIPOPROTEINS.血清脂蛋白的组成与结构研究:从极低密度人血清脂蛋白中获得的磷脂 - 蛋白质残余物的物理化学特性分析
Biochim Biophys Acta. 1964 Dec 2;84:767-9. doi: 10.1016/0926-6542(64)90040-x.
7
CONGENITAL BETA-LIPOPROTEIN DEFICIENCY: AN HEREDITARY DISORDER INVOLVING A DEFECT IN THE ABSORPTION AND TRANSPORT OF LIPIDS.先天性β-脂蛋白缺乏症:一种涉及脂质吸收和转运缺陷的遗传性疾病。
Medicine (Baltimore). 1964 May;43:347-61.
8
THE DETERMINATION OF PLASMA TRIGLYCERIDES.血浆甘油三酯的测定
Can J Biochem. 1964 Apr;42:566-70. doi: 10.1139/o64-067.
9
RED-CELL AND PLASMA LIPIDS IN ACANTHOCYTOSIS.棘红细胞增多症中的红细胞和血浆脂质
J Clin Invest. 1963 Aug;42(8):1248-60. doi: 10.1172/JCI104810.
10
Sharper separation of lipoprotein species by paper electrophoresis in albumin-containing buffer.在含白蛋白缓冲液中通过纸电泳对脂蛋白种类进行更清晰的分离。
J Lab Clin Med. 1963 Mar;61:518-28.