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与范可尼贫血相关的肺泡蛋白沉积症

Pulmonary alveolar proteinosis associated with fanconi's anemia.

作者信息

Eldar M, Shoenfeld Y, Zaizov R, Fogel R, Asherov J, Liban E, Pinkhas J

出版信息

Respiration. 1979;38(3):177-9. doi: 10.1159/000194077.

DOI:10.1159/000194077
PMID:515542
Abstract

A 16-year old patient with Fanconi's anemia developed pre-leukemia and pulmonary infiltration which was found upon autopsy to be pulmonary alveolar proteinosis. The question whether the pulmonary alveolar proteinosis was due to the marked leukopenia and an eventual defective phagocytic ability of the leukocytes is raised.

摘要

一名16岁的范可尼贫血患者发展为白血病前期,并出现肺部浸润,尸检发现为肺泡蛋白沉积症。由此引发了一个问题,即肺泡蛋白沉积症是否是由于显著的白细胞减少以及白细胞最终吞噬能力缺陷所致。

相似文献

1
Pulmonary alveolar proteinosis associated with fanconi's anemia.与范可尼贫血相关的肺泡蛋白沉积症
Respiration. 1979;38(3):177-9. doi: 10.1159/000194077.
2
[Acute leukemia in Fanconi's anemia. Report of a patient and review of the literature].
Tijdschr Kindergeneeskd. 1987 Apr;55(2):68-72.
3
Leukemia and preleukemia in Fanconi's anemia.范可尼贫血中的白血病和白血病前期
Cancer Genet Cytogenet. 1992 Feb;58(2):206-8; discussion 209. doi: 10.1016/0165-4608(92)90116-p.
4
Hepatocellular carcinoma in an 11-year-old girl with Fanconi's anemia. Report of a case and review of the literature.
Am J Pediatr Hematol Oncol. 1986 Winter;8(4):334-7. doi: 10.1097/00043426-198624000-00012.
5
[Transient erythroleukemia in the development of acute monocytic leukemia in Fanconi's anemia].
Sangre (Barc). 1982;27(5):967-71.
6
Moyamoya and Fanconi's anemia.烟雾病和范科尼贫血。
Pediatrics. 1980 Apr;65(4):804-5.
7
Preleukemia in Fanconi's anemia: hematopoietic cell multinuclearity, membrane duplication, and dysgranulogenesis.范可尼贫血中的白血病前期:造血细胞多核化、膜复制及粒细胞生成异常。
J Submicrosc Cytol. 1987 Apr;19(2):355-64.
8
The association of Fanconi's anemia and squamous cell carcinoma.范可尼贫血与鳞状细胞癌的关联。
Cancer. 1983 Sep 1;52(5):926-8. doi: 10.1002/1097-0142(19830901)52:5<926::aid-cncr2820520530>3.0.co;2-t.
9
[Myeloid leukemia during Fanconi's anemia].范可尼贫血患者的髓系白血病
Wiad Lek. 1976 Jan 15;29(2):145-50.
10
[Transformation of Fanconi's anemia into acute leukemia: apropos of 2 cases in a series of 21 patients].
Tunis Med. 1986 Aug-Sep;64(8-9):755-9.

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