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Lysosomes in type II glycogenosis. Changes during administration of extract from Aspergillus niger.

作者信息

Hug G, Schubert W K

出版信息

J Cell Biol. 1967 Oct;35(1):C1-6. doi: 10.1083/jcb.35.1.c1.

DOI:10.1083/jcb.35.1.c1
PMID:5234586
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC2107106/
Abstract
摘要

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A biochemical and ultrastructural study of liver, muscle, heart and kidney in type II glycogenosis.II型糖原贮积病肝脏、肌肉、心脏及肾脏的生化与超微结构研究
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Enzyme replacement therapy for Pompe disease.庞贝病的酶替代疗法。
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State of the art in muscle glycogenoses.肌肉糖原贮积症的最新进展。
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Enzyme therapy for pompe disease with recombinant human alpha-glucosidase from rabbit milk.用兔乳中重组人α-葡萄糖苷酶对庞贝氏病进行酶疗法。
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High-level production of recombinant human lysosomal acid alpha-glucosidase in Chinese hamster ovary cells which targets to heart muscle and corrects glycogen accumulation in fibroblasts from patients with Pompe disease.在中国仓鼠卵巢细胞中高效生产重组人溶酶体酸性α-葡萄糖苷酶，该酶靶向心肌并纠正庞贝病患者成纤维细胞中的糖原积累。
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Latency of endogenous and exogenous lysosomal glucosidases.内源性和外源性溶酶体葡萄糖苷酶的潜伏期。
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8
The genetic mismanagement of complex lipid metabolism.复杂脂质代谢的基因管理不当。
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9
Studies on the oestrogen sulphatase and arylsulphatase C activities of rat liver.大鼠肝脏雌激素硫酸酯酶和芳基硫酸酯酶C活性的研究。
Biochem J. 1972 Jun;128(2):337-45. doi: 10.1042/bj1280337.
10
The glycogen storage diseases.糖原贮积病
J Clin Pathol Suppl (R Coll Pathol). 1974;8:106-21.

本文引用的文献

1
Menghini needle biopsy of the liver.肝脏的Menghini针活检
Am J Dis Child. 1960 Jul;100:42-6. doi: 10.1001/archpedi.1960.04020040044009.
2
AN ELECTRON MICROSCOPIC AND BIOCHEMICAL STUDY OF TYPE II GLYCOGENOSIS.II型糖原贮积病的电子显微镜及生化研究
Lab Invest. 1964 Sep;13:1139-52.
3
alpha-Glucosidase deficiency in generalized glycogenstorage disease (Pompe's disease).全身性糖原贮积病（庞贝氏病）中的α-葡萄糖苷酶缺乏症。
Biochem J. 1963 Jan;86(1):11-6. doi: 10.1042/bj0860011.
4
Tissue fractionation studies. 16. Intracellular distribution and properties of alpha-glucosidases in rat liver.组织分级分离研究。16. 大鼠肝脏中α-葡萄糖苷酶的细胞内分布及特性
Biochem J. 1963 Jan;86(1):16-21. doi: 10.1042/bj0860016.
5
The action of an amyloglucosidase of Aspergillus niger on starch and malto-oligosaccharides.黑曲霉的淀粉葡萄糖苷酶对淀粉和麦芽低聚糖的作用。
J Biol Chem. 1959 Aug;234(8):1966-70.
6
Diseases of glycogen storage with special reference to the cardiac type of generalized glycogenosis.糖原贮积病，特别提及全身性糖原贮积症的心脏型。
Ann N Y Acad Sci. 1959 Feb 6;72(12):439-50. doi: 10.1111/j.1749-6632.1959.tb44172.x.
7
The liver in generalized glycogen storage disease. Light microscopic observations.
Am J Pathol. 1966 Jul;49(1):99-111.