IV型糖原贮积症。患者缺乏分支酶α-1,4-葡聚糖：α-1,4-葡聚糖6-糖基转移酶。 - Suppr

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超能文献

Type IV glycogenosis. Patient with absence of a branching enzyme alpha-1,4-glucan:alpha-1,4-glucan 6-glycosyl transferase.

作者信息

Reed G B, Dixon J F, Neustein J B, Donnell G N, Landing B H

出版信息

Lab Invest. 1968 Nov;19(5):546-57.

PMID:5247008

Abstract

摘要

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Type IV glycogenosis. Patient with absence of a branching enzyme alpha-1,4-glucan:alpha-1,4-glucan 6-glycosyl transferase.

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