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聋哑-心脏综合征及治疗观察

The surdo-cardiac syndrome and therapeutic observations.

作者信息

Olley P M, Fowler R S

出版信息

Br Heart J. 1970 Jul;32(4):467-71. doi: 10.1136/hrt.32.4.467.

DOI:10.1136/hrt.32.4.467
PMID:5433307
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC487355/
Abstract

First recognized in 1957, the surdo-cardiac syndrome includes congenital deafness, prolonged QT interval, and a high incidence of syncope and sudden death. Haemodynamic studies in two patients were normal except for an abnormal wave during left ventricular diastole probably related to abnormal left ventricular relaxation. The syncopal attacks are based on cardiac arrhythmias: both ventricular fibrillation and asystole may occur. Abnormal adrenergic stimulation of the heart is probably responsible. Propranolol appears to be effective in preventing the syncopal attacks. Artificial pacemaking provoked ventricular fibrillation in one patient and seems contraindicated.

摘要

1957年首次被发现，聋哑-心脏综合征包括先天性耳聋、QT间期延长，以及晕厥和猝死的高发生率。两名患者的血流动力学研究除左心室舒张期出现异常波（可能与左心室舒张异常有关）外均正常。晕厥发作基于心律失常：室颤和心搏停止都可能发生。心脏异常的肾上腺素能刺激可能是原因所在。普萘洛尔似乎对预防晕厥发作有效。人工起搏在一名患者中诱发了室颤，似乎是禁忌的。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/927a/487355/b0559e5fa05c/brheartj00308-0049-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/927a/487355/b3a79a2fc183/brheartj00308-0048-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/927a/487355/b8f2ed2f5114/brheartj00308-0048-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/927a/487355/4d15893b031c/brheartj00308-0049-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/927a/487355/b0559e5fa05c/brheartj00308-0049-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/927a/487355/b3a79a2fc183/brheartj00308-0048-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/927a/487355/b8f2ed2f5114/brheartj00308-0048-b.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/927a/487355/4d15893b031c/brheartj00308-0049-a.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/927a/487355/b0559e5fa05c/brheartj00308-0049-b.jpg

相似文献

1
The surdo-cardiac syndrome and therapeutic observations.聋哑-心脏综合征及治疗观察
Br Heart J. 1970 Jul;32(4):467-71. doi: 10.1136/hrt.32.4.467.
2
[Changes in ECG and cardiac rhythm with epilepsy-like attacks and sudden death in childhood. Surdo-cardiac and related syndromes].[儿童癫痫样发作及猝死时的心电图和心律变化。心聋及相关综合征]
Tidsskr Nor Laegeforen. 1974 Apr;94(10):632-5 passim.
3
[Prolonged Q-T interval and syncopal episodes, without deafness: the Romano-Ward syndrome].
G Ital Cardiol. 1972;2(2):218-25.
4
Heritable Q-T prolongation without congenital deafness (Romano-Ward syndrome).无先天性耳聋的遗传性Q-T间期延长（ Romano-Ward综合征）
Chest. 1973 Sep;64(3):359-62. doi: 10.1378/chest.64.3.359.
5
[A familial syndrome with QT time prolongation and syncopal attacks. Romano-Ward syndrome].
Med Welt. 1972 Sep 30;23(40):1377-8.
6
[Jervell's cardio-auditory syndrome and multifocal ventricular tachycardia].
Arch Mal Coeur Vaiss. 1972 Feb;65(2):261-74.
7
Convulsive syncope resulting from arrhythmia in a case of congenital deafness with ECG abnormalities.先天性耳聋伴心电图异常病例中因心律失常导致的惊厥性晕厥。
Am Heart J. 1969 Jul;78(1):81-6. doi: 10.1016/0002-8703(69)90262-2.
8
[Romano-Ward syndrome and "twist of spike". Preliminary report].
Schweiz Med Wochenschr. 1973 Feb 24;103(8):301-3.
9
Surdo-cardiac syndrome: incidence among children in schools for the deaf.聋哑心综合征：聋哑学校儿童中的发病率
Can Med Assoc J. 1971 Oct 9;105(7):718-20.
10
[Jervell, Lange-Nielsen syndrome (deaf-mutism and seve heart trouble with syncopal manifestations)].[杰韦尔-朗格-尼尔森综合征（聋哑症合并严重心脏疾病伴晕厥表现）]
Rev Laryngol Otol Rhinol (Bord). 1970 Jul-Aug;91(7):546-57.

引用本文的文献

1
Asystole in the prolonged QT syndrome.长QT综合征中的心脏停搏。
Arch Dis Child. 1984 Jun;59(6):571-3. doi: 10.1136/adc.59.6.571.
2
Surdo-cardiac syndrome: incidence among children in schools for the deaf.聋哑心综合征：聋哑学校儿童中的发病率
Can Med Assoc J. 1971 Oct 9;105(7):718-20.
3
Observation on a case of Jervell and Lange-Neilsen syndrome in an adult.一例成年患者的杰韦尔和朗格-尼尔森综合征观察报告。

本文引用的文献

1
THIORIDAZINE HYDROCHLORIDE (MELLARIL): ITS EFFECT ON THE ELECTROCARDIOGRAM AND A REPORT OF TWO FATALITIES WITH ELECTROCARDIOGRAPHIC ABNORMALITIES.盐酸硫利达嗪（美立廉）：其对心电图的影响及两例伴有心电图异常的死亡报告。
Can Med Assoc J. 1963 Sep 14;89(11):546-54.
2
Congenital deafness and cardiac arrhythmias.先天性耳聋和心律失常。
Am J Cardiol. 1967 May;19(5):627-43. doi: 10.1016/0002-9149(67)90467-5.
3
[Jervell and Lange-Nielsen syndrome. Cardiologic study of 211 deaf-mutes].[杰韦尔和朗格-尼尔森综合征。211名聋哑人的心脏病学研究]
Br Heart J. 1972 Jun;34(6):648-52. doi: 10.1136/hrt.34.6.648.
4
Sudden unexpected death in infants. Evidence on a lethal cardiac arrhythmia.婴儿猝死。关于致命性心律失常的证据。
Ulster Med J. 1973;42(2):136-52.
5
Hereditary prolongation of QT interval.遗传性QT间期延长。
Br Heart J. 1972 Jul;34(7):744-51. doi: 10.1136/hrt.34.7.744.
6
Syncope and transient loss of consciousness. Differential diagnosis and treatment.晕厥与短暂性意识丧失。鉴别诊断与治疗。
West J Med. 1975 Aug;123(2):164-70.
7
Anaesthetic considerations in the prolonged Q-T interval (LQTS): a case report.长QT间期（LQTS）的麻醉注意事项：一例病例报告。
Can Anaesth Soc J. 1979 Jan;26(1):50-4. doi: 10.1007/BF03039454.
8
A case of the cardio-auditory syndrome (long QT interval and profound deafness) diagnosed in the perinatal period and kept under surveillance for two years.一例在围产期诊断出的心脏听觉综合征（长QT间期和重度耳聋），并进行了两年的监测。
Ulster Med J. 1978;47(2):115-33.
9
Prolonged QT interval and cardiac arrhythmias in two neonates: sudden infant death syndrome in one case.两名新生儿出现QT间期延长和心律失常：其中一例为婴儿猝死综合征。
Arch Dis Child. 1979 Oct;54(10):776-9. doi: 10.1136/adc.54.10.776.
Cuore Circ. 1967 Dec;51(6):251-61.