Fitzsimons R B
Clin Exp Neurol. 1979;16:303-7.
2 cases of back curvature considered to be due to myopathy, but without associated limb weakness, are described. 1 case presented as infantile kyphosis with subsequent progression to scoliosis. There were some associated myopathic clinical features, including recurrent herniae and hip and knee contractures. The second case presented as an otherwise classical instance of Scheurmann's disease. Paraspinal muscle in both cases showed nonspecific abnormalities consistent with varieties of minimal change myopathy. EMG examination of limb muscles revealed myopathic abnormalities. These cases support the hypothesis that myopathy may underly some cases of apparently idiopathic scoliosis or kyphosis.
本文描述了2例被认为由肌病引起但无相关肢体无力的背部弯曲病例。1例表现为婴儿型脊柱后凸，随后发展为脊柱侧凸。存在一些相关的肌病临床特征，包括复发性疝以及髋部和膝部挛缩。第2例表现为典型的舒尔曼病。两例患者的椎旁肌均显示出与各种微小病变性肌病相符的非特异性异常。肢体肌肉的肌电图检查显示有肌病异常。这些病例支持了肌病可能是某些明显特发性脊柱侧凸或后凸病例的潜在病因这一假说。
